Literature DB >> 3086855

Short PR intervals and tachyarrhythmias in Fabry's disease.

J Efthimiou, J McLelland, D J Betteridge.   

Abstract

Two brothers with Fabry's disease presenting with palpitations were found to have intermittent supraventricular tachycardias. Their electrocardiograms, when symptom-free, revealed short PR intervals consistent with ventricular pre-excitation. Treatment of one of the brothers with verapamil resulted in improvement of the palpitations and reduction in frequency of the tachycardia. Recurrent supraventricular tachycardia associated with ventricular pre-excitation has not previously been described in Fabry's disease. Evidence suggests that this complication may be due to glycolipid deposition in the conducting system around the atrioventricular node.

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Year:  1986        PMID： 3086855      PMCID： PMC2418650          DOI： 10.1136/pgmj.62.726.285

Source DB:  PubMed          Journal:  Postgrad Med J        ISSN： 0032-5473            Impact factor:   2.401


  6 in total

1.  Morphology of the human atrioventricular node, with remarks pertinent to its electrophysiology.

Authors:  T N JAMES
Journal:  Am Heart J       Date:  1961-12       Impact factor: 4.749

2.  The syndrome of short P-R interval, normal QRS complex and paroxysmal rapid heart action.

Authors:  B LOWN; W F GANONG; S A LEVINE
Journal:  Circulation       Date:  1952-05       Impact factor: 29.690

3.  Accelerated atrioventricular conduction in Fabry's disease: a case report.

Authors:  J W Rowe; D G Caralis
Journal:  Angiology       Date:  1978-07       Impact factor: 3.619

4.  Electrophysiologic studies in the syndrome of short P-R interval, normal QRS complex.

Authors:  A R Caracta; A N Damato; J J Gallagher; M E Josephson; P J Varghese; S H Lau; E E Westura
Journal:  Am J Cardiol       Date:  1973-02       Impact factor: 2.778

5.  Hypertrophic obstructive cardiomyopathy due to Fabry's disease.

Authors:  W S Colucci; B H Lorell; F J Schoen; M J Warhol; W Grossman
Journal:  N Engl J Med       Date:  1982-10-07       Impact factor: 91.245

6.  Re-entrant tachycardia using two bypass tracts and excluding AV node in short PR interval, normal QRS syndrome.

Authors:  D E Ward; A J Camm; R A Spurrell
Journal:  Br Heart J       Date:  1978-10
  6 in total
  3 in total

Review 1.  Cardiac manifestations in Fabry disease.

Authors:  A Linhart; J C Lubanda; T Palecek; J Bultas; D Karetová; J Ledvinová; M Elleder; M Aschermann
Journal:  J Inherit Metab Dis       Date:  2001       Impact factor: 4.982

2.  Short P-R intervals and tachyarrhythmias in Fabry's disease.

Authors:  D Wise
Journal:  Postgrad Med J       Date:  1986-10       Impact factor: 2.401

3.  Cardiac-specific over-expression of epidermal growth factor receptor 2 (ErbB2) induces pro-survival pathways and hypertrophic cardiomyopathy in mice.

Authors:  Polina Sysa-Shah; Yi Xu; Xin Guo; Frances Belmonte; Byunghak Kang; Djahida Bedja; Scott Pin; Noriko Tsuchiya; Kathleen Gabrielson
Journal:  PLoS One       Date:  2012-08-09       Impact factor: 3.240
  3 in total

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