Literature DB >> 30852501

Parkes Weber syndrome presenting as Stewart-Bluefarb acroangiodermatitis.

Reena Sharma1, Mudita Gupta1, Suresh Thakur2, Archit Gupta3.   

Abstract

Parkes Weber syndrome (PWS) is a rare disorder characterised by arteriovenous (AV) fistula, along with capillary, lymphatic, venous malformations and limb hypertrophy. Stewart-Bluefarb syndrome is a variant of acroangiodermatitis, which is associated with congenital AV malformation/fistulas. It usually begins early in life, unilaterally over lower extremities presenting as violaceous to dusky coloured macules, papules or plaques with tendency to ulcerate. We are reporting a case of AV malformation fulfilling the triad of PWS and presenting with acroangiodermatitis. © BMJ Publishing Group Limited 2019. No commercial re-use. See rights and permissions. Published by BMJ.

Entities:  

Keywords:  congenital disorders; dermatology; hemangioma; vascular surgery

Mesh:

Year:  2019        PMID: 30852501      PMCID: PMC6424474          DOI: 10.1136/bcr-2018-227793

Source DB:  PubMed          Journal:  BMJ Case Rep        ISSN: 1757-790X


  1 in total

1.  Dusky erythematous plaques over the lower leg associated with bony deformity.

Authors:  T Dev; S Arava; N Bhari
Journal:  J Postgrad Med       Date:  2022 Jan-Mar       Impact factor: 1.476

  1 in total

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