Literature DB >> 30771411

A combined immunodeficiency with severe infections, inflammation, and allergy caused by ARPC1B deficiency.

Stefano Volpi1, Maria Pia Cicalese2, Paul Tuijnenburg3, Anton T J Tool4, Eloy Cuadrado5, Marwan Abu-Halaweh6, Hamid Ahanchian7, Raed Alzyoud8, Zeynep Coban Akdemir9, Federica Barzaghi2, Alexander Blank10, Bertrand Boisson11, Cristina Bottino12, Immacolata Brigida2, Roberta Caorsi13, Jean-Laurent Casanova14, Sabrina Chiesa13, Ivan Kingyue Chinn15, Gregor Dückers16, Anselm Enders17, Hans Christian Erichsen18, Lisa R Forbes15, Tomasz Gambin19, Marco Gattorno13, Ehsan Ghayoor Karimiani20, Silvia Giliani21, Michael S Gold22, Eva-Maria Jacobsen10, Machiel H Jansen3, Jovanka R King22, Ronald M Laxer23, James R Lupski24, Emily Mace15, Stefania Marcenaro25, Reza Maroofian26, Alexander B Meijer27, Tim Niehues16, Luigi D Notarangelo28, Jordan Orange15, Ulrich Pannicke29, Chris Pearson30, Paolo Picco31, Patrick J Quinn22, Ansgar Schulz10, Filiz Seeborg15, Asbjørg Stray-Pedersen32, Hasan Tawamie33, Ester M M van Leeuwen34, Alessandro Aiuti2, Rae Yeung35, Klaus Schwarz36, Taco W Kuijpers37.   

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Year:  2019        PMID: 30771411      PMCID: PMC6677392          DOI: 10.1016/j.jaci.2019.02.003

Source DB:  PubMed          Journal:  J Allergy Clin Immunol        ISSN: 0091-6749            Impact factor:   10.793


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  7 in total

Review 1.  Insights into immunity from clinical and basic science studies of DOCK8 immunodeficiency syndrome.

Authors:  Helen C Su; Huie Jing; Pam Angelus; Alexandra F Freeman
Journal:  Immunol Rev       Date:  2019-01       Impact factor: 12.988

2.  Disruption of Thrombocyte and T Lymphocyte Development by a Mutation in ARPC1B.

Authors:  Raz Somech; Atar Lev; Yu Nee Lee; Amos J Simon; Ortal Barel; Ginette Schiby; Camila Avivi; Iris Barshack; Michele Rhodes; Jiejing Yin; Minshi Wang; Yibin Yang; Jennifer Rhodes; Nufar Marcus; Ben-Zion Garty; Jerry Stein; Ninette Amariglio; Gideon Rechavi; David L Wiest; Yong Zhang
Journal:  J Immunol       Date:  2017-11-10       Impact factor: 5.422

3.  Impaired natural and CD16-mediated NK cell cytotoxicity in patients with WAS and XLT: ability of IL-2 to correct NK cell functional defect.

Authors:  Angela Gismondi; Loredana Cifaldi; Cinzia Mazza; Silvia Giliani; Silvia Parolini; Stefania Morrone; Jordan Jacobelli; Elisabetta Bandiera; Luigi Notarangelo; Angela Santoni
Journal:  Blood       Date:  2004-03-04       Impact factor: 22.113

4.  T-cell defects in patients with ARPC1B germline mutations account for combined immunodeficiency.

Authors:  Immacolata Brigida; Matteo Zoccolillo; Maria Pia Cicalese; Laurène Pfajfer; Federica Barzaghi; Serena Scala; Carmen Oleaga-Quintas; Jesus A Álvarez-Álvarez; Lucia Sereni; Stefania Giannelli; Claudia Sartirana; Francesca Dionisio; Luca Pavesi; Marta Benavides-Nieto; Luca Basso-Ricci; Paola Capasso; Benedetta Mazzi; Jeremie Rosain; Nufar Marcus; Yu Nee Lee; Raz Somech; Massimo Degano; Giuseppe Raiola; Roberta Caorsi; Paolo Picco; Marcela Moncada Velez; Joelle Khourieh; Andrés Augusto Arias; Aziz Bousfiha; Thomas Issekutz; Andrew Issekutz; Bertrand Boisson; Kerry Dobbs; Anna Villa; Angelo Lombardo; Benedicte Neven; Despina Moshous; Jean-Laurent Casanova; José Luis Franco; Luigi D Notarangelo; Cristina Scielzo; Stefano Volpi; Loïc Dupré; Jacinta Bustamante; Marco Gattorno; Alessandro Aiuti
Journal:  Blood       Date:  2018-09-25       Impact factor: 22.113

5.  Combined immunodeficiency with severe inflammation and allergy caused by ARPC1B deficiency.

Authors:  Taco W Kuijpers; Anton T J Tool; Ivo van der Bijl; Martin de Boer; Michel van Houdt; Iris M de Cuyper; Dirk Roos; Floris van Alphen; Karin van Leeuwen; Emma L Cambridge; Mark J Arends; Gordon Dougan; Simon Clare; Ramiro Ramirez-Solis; Steven T Pals; David J Adams; Alexander B Meijer; Timo K van den Berg
Journal:  J Allergy Clin Immunol       Date:  2016-12-10       Impact factor: 10.793

6.  A novel primary human immunodeficiency due to deficiency in the WASP-interacting protein WIP.

Authors:  Gaetana Lanzi; Daniele Moratto; Donatella Vairo; Stefania Masneri; Ottavia Delmonte; Tiziana Paganini; Silvia Parolini; Giovanna Tabellini; Cinzia Mazza; Gianfranco Savoldi; Davide Montin; Silvana Martino; Pierangelo Tovo; Itai M Pessach; Michel J Massaad; Narayanaswamy Ramesh; Fulvio Porta; Alessandro Plebani; Luigi D Notarangelo; Raif S Geha; Silvia Giliani
Journal:  J Exp Med       Date:  2012-01-09       Impact factor: 14.307

7.  Loss of the Arp2/3 complex component ARPC1B causes platelet abnormalities and predisposes to inflammatory disease.

Authors:  Walter H A Kahr; Fred G Pluthero; Abdul Elkadri; Neil Warner; Marko Drobac; Chang Hua Chen; Richard W Lo; Ling Li; Ren Li; Qi Li; Cornelia Thoeni; Jie Pan; Gabriella Leung; Irene Lara-Corrales; Ryan Murchie; Ernest Cutz; Ronald M Laxer; Julia Upton; Chaim M Roifman; Rae S M Yeung; John H Brumell; Aleixo M Muise
Journal:  Nat Commun       Date:  2017-04-03       Impact factor: 14.919

  7 in total
  30 in total

Review 1.  Molecular mechanisms of phenotypic variability in monogenic autoinflammatory diseases.

Authors:  Ivona Aksentijevich; Oskar Schnappauf
Journal:  Nat Rev Rheumatol       Date:  2021-05-25       Impact factor: 20.543

Review 2.  Monogenic autoinflammatory disorders: Conceptual overview, phenotype, and clinical approach.

Authors:  Peter A Nigrovic; Pui Y Lee; Hal M Hoffman
Journal:  J Allergy Clin Immunol       Date:  2020-11       Impact factor: 10.793

Review 3.  When Actin is Not Actin' Like It Should: A New Category of Distinct Primary Immunodeficiency Disorders.

Authors:  Evelien G G Sprenkeler; Steven D S Webbers; Taco W Kuijpers
Journal:  J Innate Immun       Date:  2020-08-26       Impact factor: 7.349

Review 4.  Moving towards a systems-based classification of innate immune-mediated diseases.

Authors:  Sinisa Savic; Emily A Caseley; Michael F McDermott
Journal:  Nat Rev Rheumatol       Date:  2020-02-27       Impact factor: 20.543

5.  Teasing out function from morphology: Similarities between primary cilia and immune synapses.

Authors:  Tiphaine Douanne; Jane C Stinchcombe; Gillian M Griffiths
Journal:  J Cell Biol       Date:  2021-05-06       Impact factor: 10.539

6.  WASp Is Crucial for the Unique Architecture of the Immunological Synapse in Germinal Center B-Cells.

Authors:  Yanan Li; Anshuman Bhanja; Arpita Upadhyaya; Xiaodong Zhao; Wenxia Song
Journal:  Front Cell Dev Biol       Date:  2021-06-14

Review 7.  Inborn errors of immunity with atopic phenotypes: A practical guide for allergists.

Authors:  Riccardo Castagnoli; Vassilios Lougaris; Giuliana Giardino; Stefano Volpi; Lucia Leonardi; Francesco La Torre; Silvia Federici; Stefania Corrente; Bianca Laura Cinicola; Annarosa Soresina; Caterina Cancrini; Gian Luigi Marseglia; Fabio Cardinale
Journal:  World Allergy Organ J       Date:  2021-02-22       Impact factor: 4.084

8.  MICAL2 enhances branched actin network disassembly by oxidizing Arp3B-containing Arp2/3 complexes.

Authors:  Chiara Galloni; Davide Carra; Jasmine V G Abella; Svend Kjær; Pavithra Singaravelu; David J Barry; Naoko Kogata; Christophe Guérin; Laurent Blanchoin; Michael Way
Journal:  J Cell Biol       Date:  2021-06-09       Impact factor: 10.539

Review 9.  Actin Dynamics at the T Cell Synapse as Revealed by Immune-Related Actinopathies.

Authors:  Loïc Dupré; Kaan Boztug; Laurène Pfajfer
Journal:  Front Cell Dev Biol       Date:  2021-06-24

10.  Cryo-EM of human Arp2/3 complexes provides structural insights into actin nucleation modulation by ARPC5 isoforms.

Authors:  Ottilie von Loeffelholz; Andrew Purkiss; Luyan Cao; Svend Kjaer; Naoko Kogata; Guillaume Romet-Lemonne; Michael Way; Carolyn A Moores
Journal:  Biol Open       Date:  2020-07-31       Impact factor: 2.643

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