| Literature DB >> 30762244 |
Eugénie Belzile1, Deana Funaro1, Julie Powell1.
Abstract
Localized vulvar bullous pemphigoid of childhood is an excessively rare variant of bullous pemphigoid and affects almost exclusively young girls of 7-12 years of age. In contrast to adult-onset bullous pemphigoid, a prompt response to potent topical corticosteroids is observed in the majority of cases, with a favorable prognosis and rare relapses. We report the case of a 7-year-old girl who presented with this condition. Our case reinforces the recognition of this rare subtype of childhood bullous pemphigoid as a distinct entity and enlightens the importance of performing a cutaneous biopsy when clinically indicated.Entities:
Keywords: bullous disease; bullous pemphigoid; immunobullous disease; mucous membrane disorders; vesiculobullous disorders; vulvar disorders
Year: 2019 PMID: 30762244 DOI: 10.1111/pde.13771
Source DB: PubMed Journal: Pediatr Dermatol ISSN: 0736-8046 Impact factor: 1.588