Literature DB >> 30630972

Co-inheritance of a-thalassemia dramatically decreases the risk of acute splenic sequestration in a large cohort of newborns with hemoglobin SC.

Paulo V Rezende1,2, André R Belisário1,2,3, Érica L Oliveira1, Jéssica A Almeida1, Larissa M M Oliveira1, Maristela B S R Muniz4, Marcos B Viana5,4.   

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Year:  2019        PMID: 30630972      PMCID: PMC6601081          DOI: 10.3324/haematol.2018.209221

Source DB:  PubMed          Journal:  Haematologica        ISSN: 0390-6078            Impact factor:   9.941


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  13 in total

1.  Hemoglobin sickle cell disease complications: a clinical study of 179 cases.

Authors:  François Lionnet; Nadjib Hammoudi; Katia Stankovic Stojanovic; Virginie Avellino; Gilles Grateau; Robert Girot; Jean-Philippe Haymann
Journal:  Haematologica       Date:  2012-02-07       Impact factor: 9.941

2.  Evidence supporting a single origin of the beta(C)-globin gene in blacks.

Authors:  C D Boehm; C E Dowling; S E Antonarakis; G R Honig; H H Kazazian
Journal:  Am J Hum Genet       Date:  1985-07       Impact factor: 11.025

3.  Hemoglobin sickle cell disease in Brazil.

Authors:  Ana Carolina Cabañas-Pedro; Josefina A P Braga; Roberta F Camilo-Araújo; Ana I M Silva; Perla Vicari; Maria Figueiredo
Journal:  Haematologica       Date:  2013-01       Impact factor: 9.941

4.  Hematologically and genetically distinct forms of sickle cell anemia in Africa. The Senegal type and the Benin type.

Authors:  R L Nagel; M E Fabry; J Pagnier; I Zohoun; H Wajcman; V Baudin; D Labie
Journal:  N Engl J Med       Date:  1985-04-04       Impact factor: 91.245

5.  Pain in sickle cell disease. Rates and risk factors.

Authors:  O S Platt; B D Thorington; D J Brambilla; P F Milner; W F Rosse; E Vichinsky; T R Kinney
Journal:  N Engl J Med       Date:  1991-07-04       Impact factor: 91.245

6.  Reticulocyte count is the most important predictor of acute cerebral ischemia and high-risk transcranial Doppler in a newborn cohort of 395 children with sickle cell anemia.

Authors:  André Rolim Belisário; Rahyssa Rodrigues Sales; Nayara Evelin Toledo; Maristela Braga de Sousa Rodrigues Muniz; Cibele Velloso-Rodrigues; Célia Maria Silva; Marcos Borato Viana
Journal:  Ann Hematol       Date:  2016-08-13       Impact factor: 3.673

7.  Outcome in hemoglobin SC disease: a four-decade observational study of clinical, hematologic, and genetic factors.

Authors:  Darleen R Powars; Alan Hiti; Emily Ramicone; Cage Johnson; Linda Chan
Journal:  Am J Hematol       Date:  2002-07       Impact factor: 10.047

8.  Clinical and hematological profile in a newborn cohort with hemoglobin SC.

Authors:  Paulo V Rezende; Millane V Santos; Gustavo F Campos; Laura L M Vieira; Maristela B Souza; André R Belisário; Celia M Silva; Marcos B Viana
Journal:  J Pediatr (Rio J)       Date:  2017-11-29       Impact factor: 2.197

9.  Whole-Genome-Sequence-Based Haplotypes Reveal Single Origin of the Sickle Allele during the Holocene Wet Phase.

Authors:  Daniel Shriner; Charles N Rotimi
Journal:  Am J Hum Genet       Date:  2018-03-08       Impact factor: 11.025

10.  Comparative study of sickle cell anemia and hemoglobin SC disease: clinical characterization, laboratory biomarkers and genetic profiles.

Authors:  Milena Magalhães Aleluia; Teresa Cristina Cardoso Fonseca; Regiana Quinto Souza; Fábia Idalina Neves; Caroline Conceição da Guarda; Rayra Pereira Santiago; Bruna Laís Almeida Cunha; Camylla Villas Boas Figueiredo; Sânzio Silva Santana; Silvana Sousa da Paz; Júnia Raquel Dutra Ferreira; Bruno Antônio Veloso Cerqueira; Marilda de Souza Gonçalves
Journal:  BMC Hematol       Date:  2017-09-15
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  1 in total

1.  The pleiotropic effects of α-thalassemia on HbSS and HbSC sickle cell disease: Reduced erythrocyte cation co-transport activity, serum erythropoietin, and transfusion burden, do not translate into increased survival.

Authors:  John N Brewin; Amina Nardo-Marino; Sara Stuart-Smith; Sara El Hoss; Anke Hanneman; John Strouboulis; Stephan Menzel; John S Gibson; David C Rees
Journal:  Am J Hematol       Date:  2022-07-18       Impact factor: 13.265

  1 in total

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