Literature DB >> 30503033

Colocolonic intussusception in an adult cystic fibrosis patient.

Adegboyega Timothy Adewale1, Steven M Rowe1, George M Solomon2.   

Abstract

PURPOSE: To raise awareness of colocolonic intussusception as a gastrointestinal complication of CF mimicking distal intestinal obstruction syndrome (DIOS) and discuss risk of recurrence. CASE
SUMMARY: A 33-year-old Caucasian male with cystic fibrosis presented with an acute abdomen diagnosed via imaging as colocolonic intussusception. He was managed with fluid replacement therapy and polyethylene glycol. He was re-admitted due to recurrence likely secondary to recurrent constipation and development of a fecalith. Surgery was contraindicated due to absence of tissue ischemia or necrosis. DISCUSSION: Several possible etiological factors have been described, especially some that tend to occur within the context of CF disease, such as DIOS and PERT, and symptoms of colocolonic intussusception are similar to those of other causes of an acute abdomen but distinguishable by advanced imaging modalities. Due to risk of recurrence, an etiology of intussusception should be sought.
CONCLUSION: Colo-colonic intussusception is a rare cause of an acute abdomen in the adult Cystic Fibrosis (CF) patient and may be associated with underlying constipation or presence of a fecalith.
Copyright © 2018. Published by Elsevier B.V.

Entities:  

Keywords:  Colocolonic intussusception; Cystic fibrosis (CF); Distal Intestinal Obstruction Syndrome (DIOS); Gastrointestinal manifestations of CF

Mesh:

Substances:

Year:  2018        PMID: 30503033      PMCID: PMC7227133          DOI: 10.1016/j.jcf.2018.11.013

Source DB:  PubMed          Journal:  J Cyst Fibros        ISSN: 1569-1993            Impact factor:   5.482


  4 in total

Review 1.  Gastrointestinal Manifestations of Cystic Fibrosis.

Authors:  Thomas Kelly; James Buxbaum
Journal:  Dig Dis Sci       Date:  2015-02-04       Impact factor: 3.199

2.  Intussusception in adults with cystic fibrosis: a case series with review of the literature.

Authors:  Edward F Nash; Anne Stephenson; Emma J Helm; Terence Ho; Chandra M Thippanna; Asad Ali; Joanna L Whitehouse; David Honeybourne; Elizabeth Tullis; Peter R Durie
Journal:  Dig Dis Sci       Date:  2011-06-16       Impact factor: 3.199

Review 3.  Distal intestinal obstruction syndrome and colonic pathologies in cystic fibrosis.

Authors:  J D Canny; A Brookes; D B Bowley
Journal:  Br J Hosp Med (Lond)       Date:  2017-01-02       Impact factor: 0.825

4.  Adult intussusception.

Authors:  T Azar; D L Berger
Journal:  Ann Surg       Date:  1997-08       Impact factor: 12.969

  4 in total
  1 in total

1.  Adult Idiopathic Ileocolonic Intussusception: A Case Report.

Authors:  Rodney C Sena; Garett Forosisky
Journal:  Cureus       Date:  2021-12-13
  1 in total

北京卡尤迪生物科技股份有限公司 © 2022-2023.