Literature DB >> 30473133

Fractures and bone health monitoring in boys with Duchenne muscular dystrophy managed within the Scottish Muscle Network.

Shuko Joseph1, Cunyi Wang2, Marina Di Marco3, Iain Horrocks4, Ishaq Abu-Arafeh5, Alex Baxter6, Nuno Cordeiro7, Linda McLellan8, Kenneth McWilliam6, Karen Naismith9, Elma Stephen10, S Faisal Ahmed11, Sze Choong Wong12.   

Abstract

There are limited reports of radiologically confirmed fractures and bone health monitoring in with Duchenne muscular dystrophy. We performed a retrospective study of 91 boys, with a median age of 11.0 years, who are currently managed in Scotland with the aim to assess the frequency of radiologically confirmed fractures and report on bone health monitoring in relation to International Care Consensus Guidance. Of these boys, 59 (65%) were receiving glucocorticoid (GC) therapy and 23 (25%) had received previous treatment. Of those currently on GC, 37 (63%) had an assessment of bone mineral density and none had routine imaging for vertebral fractures during the study period. Of the 91 boys, 44 (48%) had sustained at least one symptomatic radiographically confirmed fracture. The probability of sustaining a first symptomatic fracture was 50% by 12.8 years old (95%CI: 12.1, 13.6). The most common sites for non-vertebral fracture were the femur and tibia. In this review of boys with DMD, almost half had sustained at least one radiologically confirmed symptomatic fracture. There is a need for standardized bone health monitoring in DMD that includes routine imaging of the spine to identify vertebral fractures, given the persistence of insult to the skeleton in these boys.
Copyright © 2018. Published by Elsevier B.V.

Entities:  

Keywords:  Bone mineral density; Glucocorticoid; Osteoporosis; Skeletal fragility; Vitamin D

Mesh:

Substances:

Year:  2018        PMID: 30473133     DOI: 10.1016/j.nmd.2018.09.005

Source DB:  PubMed          Journal:  Neuromuscul Disord        ISSN: 0960-8966            Impact factor:   4.296


  5 in total

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