| Literature DB >> 30400128 |
Mikaela I Poling1, Craig R Dufresne2.
Abstract
While officially designated as distal arthrogryposis type 2A, the condition commonly referred to as Freeman-Sheldon syndrome (FSS) also historically has been termed craniocarpotarsal dystrophy, whistling face syndrome, and craniocarpotarsal dysplasia and classified at different times as a skeletal dysplasia, nonprogressive myopathy, craniofacial syndrome, and distal arthrogryposis. Having previously provided evidence for FSS being a complex myopathic craniofacial syndrome with extra-craniofacial features in most patients, the rationale for revising the FSS eponym and supplanting the current official designation with a new one was based on considerations for educational usefulness, historical accuracy, communication fluency, and nosologic clarity underpinned by genetic, pathologic, and operative experience and outcomes.Entities:
Mesh:
Year: 2018 PMID: 30400128 DOI: 10.1097/SCS.0000000000004802
Source DB: PubMed Journal: J Craniofac Surg ISSN: 1049-2275 Impact factor: 1.046