Literature DB >> 30346252

Intravascular large B-cell lymphoma presenting as an isolated cauda equina-conus medullaris syndrome - A case report.

Yang Yu1, Raghav Govindarajan1.   

Abstract

Context: Intravascular large B-cell lymphoma (IVLBCL) is a rare form of Non-Hodgkin lymphoma. The central nervous system, skin and hematopoietic system are the most commonly affected sites. We report a case of IVLBCL presenting as a combined conus medullaris-cauda equina syndrome. Findings: A 55-year-old Caucasian male presented with signs and symptoms of a combined conus medullaris-cauda equina syndrome confirmed by MRI and needle EMG. PET scan revealed a hyperactive focus in the adrenal gland, and biopsy showed evidence of IVLBCL. Therapy with R-CHOP resulted in improvement of weakness.
Conclusion: A high index of suspicion and consideration of IVLBCL in the differential for patients with these isolated spinal cord symptoms and CSF findings may help initiate early and suitable therapy which has been proven to be beneficial.

Entities:  

Keywords:  CD 20+ lymphocytes; Cauda equina; Conus medullaris; Intravascular; Lymphoma; Rituximab

Year:  2018        PMID: 30346252      PMCID: PMC7480634          DOI: 10.1080/10790268.2018.1527083

Source DB:  PubMed          Journal:  J Spinal Cord Med        ISSN: 1079-0268            Impact factor:   1.985


  10 in total

1.  An Asian variant of intravascular large B-cell lymphoma: clinical, pathological and cytogenetic approaches to diffuse large B-cell lymphoma associated with haemophagocytic syndrome.

Authors:  T Murase; S Nakamura; K Kawauchi; H Matsuzaki; C Sakai; T Inaba; K Nasu; K Tashiro; T Suchi; H Saito
Journal:  Br J Haematol       Date:  2000-12       Impact factor: 6.998

2.  Central nervous system involvement in intravascular large B-cell lymphoma: a retrospective analysis of 109 patients.

Authors:  Kazuyuki Shimada; Takuhei Murase; Kosei Matsue; Masataka Okamoto; Naoaki Ichikawa; Norifumi Tsukamoto; Nozomi Niitsu; Hiroshi Miwa; Hideki Asaoku; Hiroshi Kosugi; Ako Kikuchi; Morio Matsumoto; Yoshio Saburi; Yasufumi Masaki; Kazuhito Yamamoto; Motoko Yamaguchi; Shigeo Nakamura; Tomoki Naoe; Tomohiro Kinoshita
Journal:  Cancer Sci       Date:  2010-03-06       Impact factor: 6.716

3.  Definition, diagnosis, and management of intravascular large B-cell lymphoma: proposals and perspectives from an international consensus meeting.

Authors:  Maurilio Ponzoni; Andrés J M Ferreri; Elías Campo; Fabio Facchetti; Luca Mazzucchelli; Tadashi Yoshino; Takuhei Murase; Stefano A Pileri; Claudio Doglioni; Emanuele Zucca; Franco Cavalli; Shigeo Nakamura
Journal:  J Clin Oncol       Date:  2007-06-18       Impact factor: 44.544

4.  Rituximab monotherapy for patients with recurrent primary CNS lymphoma.

Authors:  T T Batchelor; S A Grossman; T Mikkelsen; X Ye; S Desideri; G J Lesser
Journal:  Neurology       Date:  2011-03-08       Impact factor: 9.910

5.  Intravascular lymphomatosis. A systemic disease with neurologic manifestations.

Authors:  J Glass; F H Hochberg; D C Miller
Journal:  Cancer       Date:  1993-05-15       Impact factor: 6.860

6.  The addition of rituximab to anthracycline-based chemotherapy significantly improves outcome in 'Western' patients with intravascular large B-cell lymphoma.

Authors:  Andrés J M Ferreri; Giuseppina P Dognini; Osnat Bairey; Arpad Szomor; Carlos Montalbán; Barbara Horvath; Judit Demeter; Lilj Uziel; Riccardo Soffietti; John F Seymour; Achille Ambrosetti; Rein Willemze; Maurizio Martelli; Giuseppe Rossi; Anna Candoni; Amalia De Renzo; Claudio Doglioni; Emanuele Zucca; Franco Cavalli; Maurilio Ponzoni
Journal:  Br J Haematol       Date:  2008-08-10       Impact factor: 6.998

7.  Neurologic manifestations of intravascular lymphomatosis.

Authors:  J E Chapin; L E Davis; M Kornfeld; R N Mandler
Journal:  Acta Neurol Scand       Date:  1995-06       Impact factor: 3.209

Review 8.  Intravascular lymphoma: clinical presentation, natural history, management and prognostic factors in a series of 38 cases, with special emphasis on the 'cutaneous variant'.

Authors:  Andrés J M Ferreri; Elías Campo; John F Seymour; Rein Willemze; Fiorella Ilariucci; Achille Ambrosetti; Emanuele Zucca; Giuseppe Rossi; Armando López-Guillermo; Miguel A Pavlovsky; Marie-Louise Geerts; Anna Candoni; Maurizio Lestani; Silvia Asioli; Mario Milani; Miguel A Piris; Stefano Pileri; Fabio Facchetti; Franco Cavalli; Maurilio Ponzoni
Journal:  Br J Haematol       Date:  2004-10       Impact factor: 6.998

9.  Retrospective analysis of intravascular large B-cell lymphoma treated with rituximab-containing chemotherapy as reported by the IVL study group in Japan.

Authors:  Kazuyuki Shimada; Kosei Matsue; Kazuhito Yamamoto; Takuhei Murase; Naoaki Ichikawa; Masataka Okamoto; Nozomi Niitsu; Hiroshi Kosugi; Norifumi Tsukamoto; Hiroshi Miwa; Hideki Asaoku; Ako Kikuchi; Morio Matsumoto; Yoshio Saburi; Yasufumi Masaki; Motoko Yamaguchi; Shigeo Nakamura; Tomoki Naoe; Tomohiro Kinoshita
Journal:  J Clin Oncol       Date:  2008-05-27       Impact factor: 44.544

10.  First report on a prospective trial with yttrium-90-labeled ibritumomab tiuxetan (Zevalin) in primary CNS lymphoma.

Authors:  Sofiane Maza; Philipp Kiewe; Dieter L Munz; Agnieszka Korfel; Bernd Hamm; Kristoph Jahnke; Eckhard Thiel
Journal:  Neuro Oncol       Date:  2008-12-05       Impact factor: 12.300

  10 in total
  3 in total

1.  A 52-Year-Old Man With Progressive Weakness and Incontinence.

Authors:  Ayse Altintas; Ayca Ersen Danyeli; Subutay Berke Bozkurt; Sanem Pinar Uysal; Sergin Akpek; Murat Serhat Aygun; Olga Meltem Akay; Bulent Kahyaoglu; Selcuk Peker; Umit Barbaros Ure; Burhan Ferhanoglu
Journal:  Neurohospitalist       Date:  2021-08-13

2.  Case Report: Intravascular Large B-Cell Lymphoma: A Clinicopathologic Study of Four Cases With Review of Additional 331 Cases in the Literature.

Authors:  Yingying Han; Qingjiao Li; Dan Wang; Lushan Peng; Tao Huang; Chunlin Ou; Keda Yang; Junpu Wang
Journal:  Front Oncol       Date:  2022-05-13       Impact factor: 5.738

3.  Post-mortem diagnosis of intravascular large B-cell lymphoma.

Authors:  Aniello Maiese; Raffaele La Russa; Alessandra De Matteis; Paola Frati; Vittorio Fineschi
Journal:  J Int Med Res       Date:  2020-06       Impact factor: 1.671

  3 in total

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