Leiomyoepithelioma of iris pigment epithelium.

A 4-year-old boy had a jet-black, nodular lesion growing in his right iris. Detailed clinical and histopathologic studies of this unusual tumor showed the lesion to be derived from the anterior iris pigment epithelium. The tumor cells appeared to be benign and exhibited characteristics of both pigment epithelium and smooth muscle. We have called this tumor "leiomyoepithelioma of iris pigment epithelium."