Literature DB >> 30324996

Encapsulating sclerosing peritonitis : two rare observations and literature review.

Houcine Maghrebi, Amine Makni, Rami Rhaeim, Alia Zehani, Anis Haddad, Amine Daghfous, Wael Rebai, Mohamed Jouini, Montasser Kacem, Zoubeir Ben Safta.   

Abstract

Sclerosing encapsulating peritonitis (SEP) is a rare and little known pathological entity. It is a chronic fibro-inflammatory disease of the peritoneum, resulting in the formation of a thick fibrous membrane, which engages partially or totally the abdominal organs. Clinical and radiological signs make the diagnosis difficult to establish preoperatively. We present two original observations of SEP illustrating different clinical presentations, diagnostic and therapeutic means. His diagnosis requires a peritoneal biopsy. The treatment is not completely established. Surgical treatment is difficult, involving viscerolysis and multiple incisions of the fibrous membrane. Despite the current progress in therapeutic management, the prognosis remains pejorative, with significant mortality.

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Year:  2018        PMID: 30324996

Source DB:  PubMed          Journal:  Tunis Med        ISSN: 0041-4131


  2 in total

1.  Idiopathic sclerosing encapsulating peritonitis: An uncommon cause of intestinal obstruction in a virgin abdomen.

Authors:  Asma Sghair; Mehdi Debaibi; Majdi Kchaou; Skander Talbi; Azza Sridi; Adnen Chouchen
Journal:  Clin Case Rep       Date:  2022-03-15

Review 2.  Sclerosing encapsulating peritonitis: three case reports and review of the literature.

Authors:  Zhenbin Zhang; Menglai Zhang; Ling Li
Journal:  J Int Med Res       Date:  2020-08       Impact factor: 1.671

  2 in total

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