[Changes in brain stem potentials in dystrophia myotonica].

In 15 patients with dystrophia myotonica brainstem auditory potentials (BAEP) were examined: in 8 patients (53%) pathological components in the BAEP's (such as increased latency of one peak) and in 80% a pathologic component in the neurography could be found. Comparing the latencies of the peak and the interwave latencies in the patients' and control group there was no significant difference. Hearing disturbances influenced the latencies of the first BAEP-component, increased triglycerides correlated with pathologic nerve conduction velocity and singular pathologic BAEP values correlated with abnormal neurographic parameters. All these correlations emphasize the complexity of alterations in dystrophia myotonica.