Literature DB >> 30250636

JAK inhibitors for refractory lymphoma.

Hiroshi Kimura1.   

Abstract

Entities:  

Keywords:  CAEBV; EBV; STAT3; ruxolitinib

Year:  2018        PMID: 30250636      PMCID: PMC6152482          DOI: 10.18632/oncotarget.26054

Source DB:  PubMed          Journal:  Oncotarget        ISSN: 1949-2553


× No keyword cloud information.
Epstein-Barr virus (EBV), which belongs to the gammaherpesvirus subfamily, is a ubiquitous tumor virus. EBV infects B cells via CD21 and is associated with a variety of B-cell neoplasms such as Burkitt lymphoma, EBV-positive diffuse large B-cell lymphoma, and posttransplant lymphoproliferative disorders [1]. EBV also infects T and NK cells and is associated with extranodal NK/T cell lymphoma-nasal type, aggressive NK-cell leukaemia, and EBV-positive T-cell and NK-cell lymphoproliferative diseases of childhood (EBV+ T/NK LPD) [1, 2]. Chronic active EBV infection (CAEBV), which is defined as an EBV+ T/NK LPD in the 2017 WHO classification [3], is characterised by persistent EBV infection in T/NK cells and occasional transformation to peripheral lymphoma of T/NK-cell lineage cells [2, 4, 5]. The disease has an inflammatory aspect, as hypercytokinaemia is a common feature [6]. CAEBV is a rare but intractable disease with a poor prognosis. Compared with EBV+ B-cell neoplasms, which can be treated with rituximab-containing regimens, the optimum treatment strategy for CAEBV has not yet been established. In this issue of Oncotarget, Onozawa et al. report that signal transducers and activators of transcription (STAT) 3 is constitutively active in both EBV+ T/NK cell lines and peripheral blood mononuclear cells from CAEBV patients [7]. They also show that ruxolitinib, an inhibitor of Janus kinase (JAK)1/2, suppresses not only the viability of EBV-infected T/NK cells but also their production of inflammatory cytokines. From these results, they conclude that STAT3 could be a therapeutic target for CAEBV. STAT3 is an important signalling mediator and is constitutively activated in a variety of tumours, including lymphomas. Therefore, this mediator has been investigated as a target for the treatment of many types of cancer. Interestingly, STAT3 is activated in most EBV-associated hematological and epithelial malignancies. Latent membrane protein (LMP) 1 is an oncoprotein encoded by EBV, and constitutively activates the NF-κB, PI3K/AKT, and JNK pathways [1]. LMP1 specifically interacts with JAK and activates STAT proteins, including STAT3. Moreover, activation of the JAK/STAT pathway promotes the expression of LMP1 [8]. Onozawa et al. also demonstrate that ruxolitinib inhibits the phosphorylation of constitutively active STAT3 and induces apoptosis in an EBV-positive T-cell line. We recently reported that tofacinib, a JAK3-selective inhibitor, induces G1 cell-cycle arrest and inhibits the growth of EBV-positive T/NK lymphoma cells, in which the JAK/STAT pathway is activated [9]. Whether such constitutive activation of the JAK/STAT pathway is mediated by LMP1 is of great interest, although confirmation of this would require silencing of the LMP1 gene, which is difficult, particularly in T/NK cell lines. Novel approaches involving molecular-targeted therapies are needed to establish the optimum treatment strategy for CAEBV. At present the only curative therapy is hematopoietic stem cell transplantation, but this has a high incidence of complications [4, 5]. JAK inhibitors such as ruxolitinib and tofacinib are promising candidates for this purpose, as they target the EBV-driven pathway. More importantly, these drugs are approved and in use for other diseases (ruxolitinib for myelofibrosis and polycythemia vera; tofacinib for rheumatoid arthritis); therefore, evidence of their safety is abundant. We hope that incorporation of JAK inhibitors in the treatment regimen will improve the prognosis of CAEBV, although further extensive ex vivo and in vivo studies are necessary to clarify the efficacy of these drugs.
  7 in total

Review 1.  Pathogenesis of chronic active Epstein-Barr virus infection: is this an infectious disease, lymphoproliferative disorder, or immunodeficiency?

Authors:  Hiroshi Kimura
Journal:  Rev Med Virol       Date:  2006 Jul-Aug       Impact factor: 6.989

2.  EBV-associated T/NK-cell lymphoproliferative diseases in nonimmunocompromised hosts: prospective analysis of 108 cases.

Authors:  Hiroshi Kimura; Yoshinori Ito; Shinji Kawabe; Kensei Gotoh; Yoshiyuki Takahashi; Seiji Kojima; Tomoki Naoe; Shinichi Esaki; Atsushi Kikuta; Akihisa Sawada; Keisei Kawa; Koichi Ohshima; Shigeo Nakamura
Journal:  Blood       Date:  2011-11-16       Impact factor: 22.113

3.  Epstein-Barr virus-associated lymphoproliferative disease in non-immunocompromised hosts: a status report and summary of an international meeting, 8-9 September 2008.

Authors:  J I Cohen; H Kimura; S Nakamura; Y-H Ko; E S Jaffe
Journal:  Ann Oncol       Date:  2009-06-10       Impact factor: 32.976

4.  A positive autoregulatory loop of LMP1 expression and STAT activation in epithelial cells latently infected with Epstein-Barr virus.

Authors:  Honglin Chen; Lindsey Hutt-Fletcher; Liang Cao; S Diane Hayward
Journal:  J Virol       Date:  2003-04       Impact factor: 5.103

5.  Tofacitinib induces G1 cell-cycle arrest and inhibits tumor growth in Epstein-Barr virus-associated T and natural killer cell lymphoma cells.

Authors:  Shotaro Ando; Jun-Ichi Kawada; Takahiro Watanabe; Michio Suzuki; Yoshitaka Sato; Yuka Torii; Masato Asai; Fumi Goshima; Takayuki Murata; Norio Shimizu; Yoshinori Ito; Hiroshi Kimura
Journal:  Oncotarget       Date:  2016-11-22

6.  STAT3 is constitutively activated in chronic active Epstein-Barr virus infection and can be a therapeutic target.

Authors:  Erika Onozawa; Haruna Shibayama; Honami Takada; Ken-Ichi Imadome; Sho Aoki; Mayumi Yoshimori; Norio Shimizu; Shigeyoshi Fujiwara; Takatoshi Koyama; Osamu Miura; Ayako Arai
Journal:  Oncotarget       Date:  2018-07-24

Review 7.  Chronic Active Epstein-Barr Virus Disease.

Authors:  Hiroshi Kimura; Jeffrey I Cohen
Journal:  Front Immunol       Date:  2017-12-22       Impact factor: 7.561

  7 in total

北京卡尤迪生物科技股份有限公司 © 2022-2023.