Literature DB >> 30218977

Notch pathway inhibition with LY3039478 in soft tissue sarcoma and gastrointestinal stromal tumours.

Olivier Mir1, Analia Azaro2, Jaime Merchan3, Rashmi Chugh4, Jonathan Trent3, Jordi Rodon5, Ute Ohnmacht6, J T Diener6, Claire Smith7, Eunice Yuen7, Gerard Joseph Oakley6, Axel Le Cesne1, Jean-Charles Soria1, Karim A Benhadji6, Christophe Massard8.   

Abstract

BACKGROUND: LY3039478 is an orally bioavailable selective Notch inhibitor. This phase 1a/b trial evaluated the safety, pharmacokinetics and antitumour activity of LY3039478 in patients with soft tissue sarcoma (STS) and gastrointestinal stromal tumour (GIST).
METHODS: This multipart, phase 1 trial enrolled patients with refractory advanced/metastatic STS and GIST, measurable disease, Eastern Cooperative Oncology Group ≤1 and baseline tumour tissue. Eligible patients received LY3039478 50mg/75 mg three times per week, for 28-day cycle until disease progression. Safety assessments were based on Common Terminology Criteria for Adverse Events, V4.0. Tumour responses were assessed using Response Evaluation Criteria in Solid Tumours (RECIST 1.1) and Choi criteria. Primary objectives were to confirm the recommended phase 2 dose of LY3039478 and document the antitumour activity. Secondary objectives were safety and toxicity, pharmacokinetics (PK), progression-free survival (PFS) and overall survival (OS).
RESULTS: Sixty-nine patients were enrolled and received LY3039478 (27 males, 42 females; median age 58, range 31-78). 16/37 (43%) patients with evaluable samples were positive for Notch 1 immunohistochemistry. Per RECIST 1.1, in leiomyosarcoma (LMS) group (n = 29), ten (36%) had stable disease (SD) and one (4%) had unconfirmed partial response (PR). In GIST group (n = 13), four (31%) had SD. Among other STS subtypes (n = 27), one patient with angiosarcoma had unconfirmed PR, six (21%) had SD. Median PFS was 1.9 months (95% confidence interval:1.6-3.3) for LMS, 1.9 months (0.3-6.1) for GIST and 1.7 months (1.4-2.2) for other STS groups. Median OS was 7.4 months (4.3-non-evaluable [NE]) for LMS, 16.5 months (3.9-16.5) for GIST and 5.6 months (3.4-NE) for other STS groups. Most common adverse events were diarrhoea, nausea, vomiting and decreased appetite.
CONCLUSION: LY3039478 suggested a modest clinical activity in patients with STS and GIST and had a manageable safety profile.
Copyright © 2018 Elsevier Ltd. All rights reserved.

Entities:  

Keywords:  Angiosarcoma; Gastrointestinal stromal tumours; Leiomyosarcoma; Liposarcoma; Notch inhibitor; Pleomorphic sarcoma; Rhabdomyosarcoma; Soft tissue sarcoma

Mesh:

Substances:

Year:  2018        PMID: 30218977     DOI: 10.1016/j.ejca.2018.08.012

Source DB:  PubMed          Journal:  Eur J Cancer        ISSN: 0959-8049            Impact factor:   9.162


  10 in total

1.  Gamma Secretase Inhibitors as Potential Therapeutic Targets for Notch Signaling in Uterine Leiomyosarcoma.

Authors:  Yasmin Abedin; Sofia Gabrilovich; Emily Alpert; Erica Rego; Salma Begum; Qingshi Zhao; Debra Heller; Mark H Einstein; Nataki C Douglas
Journal:  Int J Mol Sci       Date:  2022-05-26       Impact factor: 6.208

Review 2.  Top Notch Targeting Strategies in Cancer: A Detailed Overview of Recent Insights and Current Perspectives.

Authors:  Gillian Moore; Stephanie Annett; Lana McClements; Tracy Robson
Journal:  Cells       Date:  2020-06-20       Impact factor: 6.600

Review 3.  Targeting cancer stem cells in drug discovery: Current state and future perspectives.

Authors:  Fang-Yu Du; Qi-Fan Zhou; Wen-Jiao Sun; Guo-Liang Chen
Journal:  World J Stem Cells       Date:  2019-07-26       Impact factor: 5.326

4.  Safety and clinical activity of the Notch inhibitor, crenigacestat (LY3039478), in an open-label phase I trial expansion cohort of advanced or metastatic adenoid cystic carcinoma.

Authors:  C Even; U Lassen; J Merchan; C Le Tourneau; J-C Soria; C Ferte; F Ricci; J T Diener; E Yuen; C Smith; G J Oakley; K A Benhadji; Christophe Massard
Journal:  Invest New Drugs       Date:  2019-04-06       Impact factor: 3.850

5.  NKX6-1 mediates cancer stem-like properties and regulates sonic hedgehog signaling in leiomyosarcoma.

Authors:  Po-Hsuan Su; Rui-Lan Huang; Hung-Cheng Lai; Lin-Yu Chen; Yu-Chun Weng; Chih-Chien Wang; Chia-Chun Wu
Journal:  J Biomed Sci       Date:  2021-04-27       Impact factor: 8.410

Review 6.  An overview of agents and treatments for PDGFRA-mutated gastrointestinal stromal tumors.

Authors:  Yingchao Sun; Lei Yue; Pengfu Xu; Weiling Hu
Journal:  Front Oncol       Date:  2022-08-31       Impact factor: 5.738

Review 7.  Genetics, epigenetics and redox homeostasis in rhabdomyosarcoma: Emerging targets and therapeutics.

Authors:  Ananya Pal; Hsin Yao Chiu; Reshma Taneja
Journal:  Redox Biol       Date:  2019-01-25       Impact factor: 11.799

Review 8.  Notch Transduction in Non-Small Cell Lung Cancer.

Authors:  Amnah Sharif; Ann Shaji; May Chammaa; Eileen Pawlik; Rodrigo Fernandez-Valdivia
Journal:  Int J Mol Sci       Date:  2020-08-08       Impact factor: 5.923

9.  A phase 1 study of crenigacestat (LY3039478), the Notch inhibitor, in Japanese patients with advanced solid tumors.

Authors:  Toshihiko Doi; Masaomi Tajimi; Joji Mori; Hiroya Asou; Koichi Inoue; Karim A Benhadji; Yoichi Naito
Journal:  Invest New Drugs       Date:  2020-09-16       Impact factor: 3.850

Review 10.  Notch signaling pathway: architecture, disease, and therapeutics.

Authors:  Binghan Zhou; Wanling Lin; Yaling Long; Yunkai Yang; Huan Zhang; Kongming Wu; Qian Chu
Journal:  Signal Transduct Target Ther       Date:  2022-03-24
  10 in total

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