Literature DB >> 30192635

Is Cystic Fibrosis-related Diabetes Reversible? New Data on CFTR Potentiation and Insulin Secretion.

Andrew W Norris1.   

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Year:  2019        PMID: 30192635      PMCID: PMC6363979          DOI: 10.1164/rccm.201808-1501ED

Source DB:  PubMed          Journal:  Am J Respir Crit Care Med        ISSN: 1073-449X            Impact factor:   21.405


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  13 in total

1.  Resolution of cystic fibrosis-related diabetes with ivacaftor therapy.

Authors:  Don Hayes; Karen S McCoy; Shahid I Sheikh
Journal:  Am J Respir Crit Care Med       Date:  2014-09-01       Impact factor: 21.405

2.  Islet Hormone and Incretin Secretion in Cystic Fibrosis after Four Months of Ivacaftor Therapy.

Authors:  Andrea Kelly; Diva D De Leon; Saba Sheikh; Devaney Camburn; Christina Kubrak; Amy J Peleckis; Darko Stefanovski; Denis Hadjiliadis; Michael R Rickels; Ronald C Rubenstein
Journal:  Am J Respir Crit Care Med       Date:  2019-02-01       Impact factor: 21.405

3.  Diabetes mellitus in cystic fibrosis is characterized by islet amyloidosis.

Authors:  M Couce; T D O'Brien; A Moran; P C Roche; P C Butler
Journal:  J Clin Endocrinol Metab       Date:  1996-03       Impact factor: 5.958

4.  Ivacaftor for the p.Ser549Arg (S549R) gating mutation - The Israeli experience.

Authors:  Adi Dagan; Malena Cohen-Cymberknoh; Michal Shteinberg; Hagit Levine; Daphna Vilozni; Yael Bezalel; Bat-El Bar Aluma; Ifat Sarouk; Moshe Ashkenazi; Moran Lavie; Reuven Tsabari; Hannah Blau; Eitan Kerem; Lea Bentur; Ori Efrati; Galit Livnat
Journal:  Respir Med       Date:  2017-09-01       Impact factor: 3.415

5.  Islet Interleukin-1β Immunoreactivity Is an Early Feature of Cystic Fibrosis That May Contribute to β-Cell Failure.

Authors:  Rebecca L Hull; Ronald L Gibson; Sharon McNamara; Gail H Deutsch; Corinne L Fligner; Charles W Frevert; Bonnie W Ramsey; Srinath Sanda
Journal:  Diabetes Care       Date:  2018-02-01       Impact factor: 19.112

6.  Insulin secretion improves in cystic fibrosis following ivacaftor correction of CFTR: a small pilot study.

Authors:  Melena D Bellin; Theresa Laguna; Janice Leschyshyn; Warren Regelmann; Jordan Dunitz; JoAnne Billings; Antoinette Moran
Journal:  Pediatr Diabetes       Date:  2013-03-13       Impact factor: 4.866

7.  Effect of Lumacaftor/Ivacaftor on glucose metabolism and insulin secretion in Phe508del homozygous cystic fibrosis patients.

Authors:  Jan C Thomassen; Matthias I Mueller; Miguel A Alejandre Alcazar; Ernst Rietschel; Silke van Koningsbruggen-Rietschel
Journal:  J Cyst Fibros       Date:  2017-12-15       Impact factor: 5.482

8.  CFTR Influences Beta Cell Function and Insulin Secretion Through Non-Cell Autonomous Exocrine-Derived Factors.

Authors:  Xingshen Sun; Yaling Yi; Weiliang Xie; Bo Liang; Michael C Winter; Nan He; Xiaoming Liu; Meihui Luo; Yu Yang; Katie Larson Ode; Aliye Uc; Andrew W Norris; John F Engelhardt
Journal:  Endocrinology       Date:  2017-10-01       Impact factor: 4.736

9.  CFTR potentiator therapy ameliorates impaired insulin secretion in CF patients with a gating mutation.

Authors:  Reuven Tsabari; Hila Iron Elyashar; Malena Cohen Cymberknowh; Oded Breuer; Shoshana Armoni; Galit Livnat; Eitan Kerem; David Haim Zangen
Journal:  J Cyst Fibros       Date:  2015-11-04       Impact factor: 5.482

10.  Structural abnormalities in islets from very young children with cystic fibrosis may contribute to cystic fibrosis-related diabetes.

Authors:  Marika Bogdani; Scott M Blackman; Cecilia Ridaura; Jean-Pierre Bellocq; Alvin C Powers; Lydia Aguilar-Bryan
Journal:  Sci Rep       Date:  2017-12-08       Impact factor: 4.379

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  6 in total

Review 1.  Update in Cystic Fibrosis 2018.

Authors:  Bonnie W Ramsey; Gregory P Downey; Christopher H Goss
Journal:  Am J Respir Crit Care Med       Date:  2019-05-15       Impact factor: 21.405

2.  Sustained Glycemic Control With Ivacaftor in Cystic Fibrosis-Related Diabetes.

Authors:  Francis Christian; Andrew Thierman; Erin Shirley; Karen Allen; Cory Cross; Kellie Jones
Journal:  J Investig Med High Impact Case Rep       Date:  2019 Jan-Dec

Review 3.  Inhaled Biologicals for the Treatment of Cystic Fibrosis.

Authors:  Valentina Sala; Alessandra Murabito; Alessandra Ghigo
Journal:  Recent Pat Inflamm Allergy Drug Discov       Date:  2019

Review 4.  Cystic Fibrosis-Related Diabetes (CFRD): Overview of Associated Genetic Factors.

Authors:  Fernanda Iafusco; Giovanna Maione; Francesco Maria Rosanio; Enza Mozzillo; Adriana Franzese; Nadia Tinto
Journal:  Diagnostics (Basel)       Date:  2021-03-22

5.  A Hyperglycemic Microenvironment Inhibits Tendon-to-Bone Healing through the let-7b-5p/CFTR Pathway.

Authors:  Tianyi Cao; Junyi Hong; Feicheng Qi; Bo Zheng; Guofang Chen; Binjia Yu; Fusheng Ye
Journal:  Comput Math Methods Med       Date:  2022-01-27       Impact factor: 2.238

Review 6.  A tale of two pancreases: exocrine pathology and endocrine dysfunction.

Authors:  Michael R Rickels; Andrew W Norris; Rebecca L Hull
Journal:  Diabetologia       Date:  2020-09-07       Impact factor: 10.122

  6 in total

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