Literature DB >> 29994846

Treatment of Apert Hand Syndrome: Strategies for Achieving a Five-Digit Hand.

Cassio Eduardo Raposo-Amaral1, Rafael Denadai1, Pedro Furlan1, Cesar Augusto Raposo-Amaral1.   

Abstract

BACKGROUND: Apert hand reconstruction requires complex surgical planning. The purpose of this study was to describe the authors' 8-year surgical experience with Apert syndrome hand reconstruction, and provide specific surgical strategies for achieving a five-digit hand in Upton type I and II hands.
METHODS: A retrospective analysis of consecutive Apert syndrome patients who underwent web-space releases between 2007 and 2015 was performed. Demographic, surgical, and outcome data were verified through medical records, clinical photographs, radiographic images, and patient interviews.
RESULTS: A total of 41 Apert syndrome patients [23 boys (56.1 percent) and 18 girls (43.9 percent)] have been treated at our hospital since 2007. A five-digit hand was achieved in all patients (100 percent) with Upton type I and II hands, and in eight patients (72.7 percent) with Upton type III hands. A four-digit hand was obtained in three of 11 patients (27.3 percent) with Upton type III hands. Four of 20 patients (25 percent) with Upton type I hands, three of 10 patients (30 percent) with Upton type II hands, and six of 11 patients (54.5 percent) with Upton type III hands required subsequent revision for aesthetic reasons.
CONCLUSIONS: Upton type III hands have demonstrated higher revision rates than type I and II hands, regardless of whether a four- or five-digit hand is obtained. Treatment strategies for Apert syndrome hands based on hand type are offered to guide four-web-space release in all patients with Upton type I and II hands. CLINICAL QUESTION/LEVEL OF EVIDENCE: Therapeutic, IV.

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Year:  2018        PMID: 29994846     DOI: 10.1097/PRS.0000000000004815

Source DB:  PubMed          Journal:  Plast Reconstr Surg        ISSN: 0032-1052            Impact factor:   4.730


  4 in total

1.  Syndrome-related outcomes following posterior vault distraction osteogenesis.

Authors:  Cassio Eduardo Raposo-Amaral; Yuri Moresco de Oliveira; Rafael Denadai; Cesar Augusto Raposo-Amaral; Enrico Ghizoni
Journal:  Childs Nerv Syst       Date:  2021-04-18       Impact factor: 1.475

2.  Severe craniolacunae and upper and lower extremity anomalies resulting from Crouzon syndrome, FGFR2 mutation, and Ser347Cys variant.

Authors:  Cassio Eduardo Raposo-Amaral; Yuri Moresco Oliveira; Rafael Denadai; Cesar Augusto Raposo-Amaral; Enrico Ghizoni
Journal:  Childs Nerv Syst       Date:  2021-01-06       Impact factor: 1.475

3.  Hand Function in Apert Syndrome.

Authors:  Cassio Eduardo Raposo-Amaral; Rafael Denadai; Thais Miguel do Monte Lameiro; Yuri Moresco de Oliveira; Cesar Augusto Raposo-Amaral
Journal:  Plast Reconstr Surg Glob Open       Date:  2019-05-01

4.  Pfeiffer Syndrome: A Therapeutic Algorithm Based on a Modified Grading Scale.

Authors:  Cassio Eduardo Raposo-Amaral; Rafael Denadai; Geiza Máximo; Cesar Augusto Raposo-Amaral; Enrico Ghizoni
Journal:  Plast Reconstr Surg Glob Open       Date:  2020-04-29
  4 in total

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