Literature DB >> 29963400

Unilateral pulmonary vein atresia without anomalous connection in adult patient with recurrent severe hemoptysis.

Andrea Dell'Amore1, Alessio Campisi1, Stefano Congiu1, Domenica Giunta1, Giampiero Dolci1, Fabio Niro1.   

Abstract

Isolated unilateral pulmonary vein atresia (UPVA) is a rare congenital malformation and the management remains controversial. In adults, pneumonectomy is the treatment of choice when significant hemoptysis becomes life-threatening. We report a case of a 28-year-old male with isolated unilateral right atresia of the pulmonary vein who had life-threatening hemoptysis treated with bronchial arteries embolization followed by successful right pneumonectomy.

Entities:  

Keywords:  Pulmonary vein atresia; congenital; hemoptysis; pneumonectomy; pulmonary vascular disease

Year:  2018        PMID: 29963400      PMCID: PMC5994435          DOI: 10.21037/jovs.2018.05.03

Source DB:  PubMed          Journal:  J Vis Surg        ISSN: 2221-2965


  5 in total

1.  Isolated unilateral pulmonary vein atesia in adults.

Authors:  M Teresa Gómez Hernández; María Rodríguez Pérez; Marcelo F Jiménez
Journal:  Arch Bronconeumol       Date:  2014-12-22       Impact factor: 4.872

Review 2.  Isolated unilateral pulmonary vein atresia in adult patients: a case report and literature review.

Authors:  Min Zhang; Qing-Chen Wu; Cheng Zhang; Qiang Li; Ying-Jiu Jiang; Dan Chen
Journal:  Heart Surg Forum       Date:  2010-12       Impact factor: 0.676

3.  Congenital unilateral pulmonary vein atresia: radiologic findings in three adult patients.

Authors:  L E Heyneman; R L Nolan; J K Harrison; H P McAdams
Journal:  AJR Am J Roentgenol       Date:  2001-09       Impact factor: 3.959

Review 4.  Congenital unilateral pulmonary venous atresia: definitive diagnosis and treatment.

Authors:  K K Pourmoghadam; J W Moore; M Khan; E M Geary; N Madan; B J Wolfson; J P de Chadarevian; D S Holsclaw; M L Jacobs
Journal:  Pediatr Cardiol       Date:  2002-09-25       Impact factor: 1.655

5.  Unilateral pulmonary vein atresia: A rare case of hemoptysis.

Authors:  Cindy S DeMastes-Crabtree; Edward Kim; Ronald L Morton
Journal:  Respir Med Case Rep       Date:  2015-05-22
  5 in total

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