Literature DB >> 29887601

Ivacaftor CFTR Potentiator Therapy is Efficient for Pancreatic Manifestations in Cystic Fibrosis.

Ilias Kounis1,1, Philippe Lévy1,1, Vinciane Rebours1,1.   

Abstract

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Year:  2018        PMID: 29887601     DOI: 10.1038/s41395-018-0123-7

Source DB:  PubMed          Journal:  Am J Gastroenterol        ISSN: 0002-9270            Impact factor:   10.864


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  7 in total

1.  Acute Recurrent and Chronic Pancreatitis as Initial Manifestations of Cystic Fibrosis and Cystic Fibrosis Transmembrane Conductance Regulator-Related Disorders.

Authors:  Christina Baldwin; Melissa Zerofsky; Meghana Sathe; David M Troendle; Emily R Perito
Journal:  Pancreas       Date:  2019-08       Impact factor: 3.327

2.  Cystic Fibrosis Transmembrane Conductance Regulator Modulator Use Is Associated With Reduced Pancreatitis Hospitalizations in Patients With Cystic Fibrosis.

Authors:  Mitchell L Ramsey; Yevgeniya Gokun; Lindsay A Sobotka; Michael R Wellner; Kyle Porter; Stephen E Kirkby; Susan S Li; Georgios I Papachristou; Somashekar G Krishna; Peter P Stanich; Phil A Hart; Darwin L Conwell; Luis F Lara
Journal:  Am J Gastroenterol       Date:  2021-12-01       Impact factor: 10.864

3.  Pancreatic Insufficiency in a Child with p.Gly542* and c.2657+5G>A Heterozygote CFTR: A Case Report.

Authors:  Fernanda Dos Anjos; Jonatha Wruck; Thiago Inácio Teixeira do Carmo; Victor Emanuel Miranda Soares; Débora Tavares de Resende E Silva; Margarete Dulce Bagatini; Sarah Franco Vieira de Oliveira Maciel
Journal:  Clin Med Res       Date:  2022-02-07

Review 4.  Central role of the sentinel acute pancreatitis event (SAPE) model in understanding recurrent acute pancreatitis (RAP): Implications for precision medicine.

Authors:  David C Whitcomb
Journal:  Front Pediatr       Date:  2022-08-15       Impact factor: 3.569

Review 5.  New Therapies to Correct the Cystic Fibrosis Basic Defect.

Authors:  Christelle Bergeron; André M Cantin
Journal:  Int J Mol Sci       Date:  2021-06-08       Impact factor: 5.923

Review 6.  Pancreatic complications in children with cystic fibrosis.

Authors:  Zachary M Sellers
Journal:  Curr Opin Pediatr       Date:  2020-10       Impact factor: 2.893

Review 7.  The Extrapulmonary Effects of Cystic Fibrosis Transmembrane Conductance Regulator Modulators in Cystic Fibrosis.

Authors:  Valentine Sergeev; Frank Y Chou; Grace Y Lam; Christopher Michael Hamilton; Pearce G Wilcox; Bradley S Quon
Journal:  Ann Am Thorac Soc       Date:  2020-02
  7 in total

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