Alba Marina Milá de la Roca-Morales1, Joan F Andreo-Marroig2, Sofía Santos-Pérez3, Andrés Soto-Varela3. 1. Department of Otorhinolaryngology, Santa Bárbara Hospital, Puertollano, Spain. 2. Department of Otorhinolaryngology, Manacor Hospital, Manacor, Spain. 3. Department of Otorhinolaryngology, University Hospital Complex of Santiago De Compostela, Santiago De Compostela, Spain.
Abstract
OBJECTIVE: To describe the pattern of dynamic posturography or its role in diagnosis in patients with cerebellar ataxia with neuropathy and vestibular arreflexia syndrome (CANVAS). MATERIALS AND METHODS: We present and describe posturographic data of four patients diagnosed with the CANVAS syndrome in a tertiary hospital. RESULTS: In all patients, the average balance score was diminished. Two patients presented a pattern of visual dependence. The other two showed misuse of three posturography sensory information (visual, vestibular and propioceptive information), specially null use of vestibular information, deterioration of somatosensory input, and poor use of strategies, particularly in conditions 5 and 6. CONCLUSIONS: If there is misuse of somatosensory information in sensory organization test (SOT) in a patient with bilateral vestibular deficit, a possibility of CANVAS should be considered. The SOT provides valuable information, because it evaluates sensory inputs influence the maintenance of balance.
OBJECTIVE: To describe the pattern of dynamic posturography or its role in diagnosis in patients with cerebellar ataxia with neuropathy and vestibular arreflexia syndrome (CANVAS). MATERIALS AND METHODS: We present and describe posturographic data of four patients diagnosed with the CANVAS syndrome in a tertiary hospital. RESULTS: In all patients, the average balance score was diminished. Two patients presented a pattern of visual dependence. The other two showed misuse of three posturography sensory information (visual, vestibular and propioceptive information), specially null use of vestibular information, deterioration of somatosensory input, and poor use of strategies, particularly in conditions 5 and 6. CONCLUSIONS: If there is misuse of somatosensory information in sensory organization test (SOT) in a patient with bilateral vestibular deficit, a possibility of CANVAS should be considered. The SOT provides valuable information, because it evaluates sensory inputs influence the maintenance of balance.
Authors: David J Szmulewicz; John A Waterston; Hamish G MacDougall; Stuart Mossman; Andrew M Chancellor; Catriona A McLean; Saumil Merchant; Peter Patrikios; G Michael Halmagyi; Elsdon Storey Journal: Ann N Y Acad Sci Date: 2011-09 Impact factor: 5.691
Authors: David J Szmulewicz; Leslie Roberts; Catriona A McLean; Hamish G MacDougall; G Michael Halmagyi; Elsdon Storey Journal: Neurol Clin Pract Date: 2016-02
Authors: D J Szmulewicz; J A Waterston; G M Halmagyi; S Mossman; A M Chancellor; C A McLean; E Storey Journal: Neurology Date: 2011-05-31 Impact factor: 9.910
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