Divya A Chari1, Dylan K Chan1. 1. Department of Otolaryngology - Head and Neck Surgery, University of California San Francisco, San Francisco, CA, USA.
Abstract
PURPOSE OF REVIEW: The aim of this report is to review current literature regarding the work-up and management of congenital sensorineural hearing loss. RECENT FINDINGS: Diagnostic evaluation of a newborn with sensorineural hearing loss begins with a complete audiologic evaluation and comprehensive history and physical exam. This review presents a diagnostic algorithm for the work-up of congenital hearing loss, focusing on the three following modalities: cytomegalovirus testing, genetic evaluation, and imaging. SUMMARY: Newborn hearing loss is a common problem and may be attributed to genetic and non-genetic factors. Complete diagnostic evaluation and treatment are essential for preventing delays in language development. Treatment consists of early intervention services and consideration of hearing aid amplification and cochlear implantation.
PURPOSE OF REVIEW: The aim of this report is to review current literature regarding the work-up and management of congenital sensorineural hearing loss. RECENT FINDINGS: Diagnostic evaluation of a newborn with sensorineural hearing loss begins with a complete audiologic evaluation and comprehensive history and physical exam. This review presents a diagnostic algorithm for the work-up of congenital hearing loss, focusing on the three following modalities: cytomegalovirus testing, genetic evaluation, and imaging. SUMMARY: Newborn hearing loss is a common problem and may be attributed to genetic and non-genetic factors. Complete diagnostic evaluation and treatment are essential for preventing delays in language development. Treatment consists of early intervention services and consideration of hearing aid amplification and cochlear implantation.
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