Literature DB >> 29744315

Oxidative Stress in Diabetic Patients with Sickle-Cell Anemia: A Warning Call for Endemic Areas.

Rajiv Mahajan1.   

Abstract

Entities:  

Year:  2018        PMID: 29744315      PMCID: PMC5932925          DOI: 10.4103/ijabmr.IJABMR_104_18

Source DB:  PubMed          Journal:  Int J Appl Basic Med Res        ISSN: 2229-516X


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Sickle-cell disease (SCD) is an inherited condition in which red blood cells (RBCs) become less flexible and some become buckled into the characteristic sickle shape.[1] SCD has been known by its symptoms of bone pains and early death for over a century in Africa.[2] Sickle cells were first identified in a medical student from Grenada.[3] In the presence of gene for sickle hemoglobin (HbS), valine, normally present at the sixth position from the amino terminus of the β chain of HbS is substituted by glutamic acid. SCD is acquired by inheriting abnormal genes from both parents. The combination from both parents can give rise to different forms of SCD; with most common at birth being homozygous sickle-cell (SS) disease, also called sickle-cell anemia, in which the HbS gene is inherited from both parents. Carrier state or sickle-cell trait (SCT) results from inheritance of an HbS gene from one parent and normal β-globin gene from the other.[1] Major clinical manifestations in patients of SCD are due to two basic mechanisms – hemolysis and vasoocclusion. The lifespan of a RBC is decreased from a normal 120 days to 10–12 days in most patients with SS disease causing megaloblastic erythropoiesis, aplastic crisis, jaundice, and gall stones. Similarly, obstruction to normal flow of blood by stiff or sickled red cells can cause ischemic changes in the area supplied and depends on the type of vessel affected.[4] On the other hand, oxidative stress is thought to exacerbate the symptoms of hemolytic anemias including sickle-cell anemia, thalassemia, glucose-6-phosphate dehydrogenase deficiency, and hereditary spherocytosis.[5] It has been reported that the oxidative stress is a major outcome of diabetes mellitus (DM) affecting red cell antioxidant enzymes, and this in turn can lead to reduced hemoglobin concentrations in diabetic patients.[6] It has also been documented that oxidative stress is an important feature of SCD and plays a significant role in the pathophysiology of hemolysis, vasoocclusion, and ensuing organ damage in sickle-cell patients.[7] A comparative study conducted on healthy individuals (CONT), individuals with type 2 DM (T2DM) or SCT, and patients with both T2DM and SCT (T2DM-SCT), comparing vascular function, hemorheological profile, and biomarkers of oxidative stress, inflammation, and nitric oxide metabolism found that oxidative stress, advanced glycation end products, and inflammation (interleukin-1 β) were greater in patients with T2DM-SCT compared with the other groups. Blood viscosity was higher in individuals with TD2M, SCT carriers, and individuals with T2DM-SCT, and the values were further increased in the latter group, thus concluding that SCT should be viewed as a risk factor for further cardiovascular disorders in individuals with T2DM.[8] In another study, normoglycemic patients with SCD demonstrated impaired β-cell function with reduced insulin secretion even before oral glucose tolerance test was impaired.[9] To make the matter worse, another study has postulated a role of elevated oxidative products in the development of insulin resistance and high glucose levels in SCD patients.[10] Thus, the cascade of diabetes leading to oxidative stress leading to hemolysis appears intermingled in patients with SCD will prove catastrophic in patients with SCD comorbid with DM and will particularly affect endemic areas. Recent epidemiological data predict that as per current trends, Africa, and more particularly sub-Saharan countries, will have the greatest increase in the number of people with T2DM, from 19.8 million in 2013 to 41.4 million in 2035.[11] As we know, in sub-Saharan African countries, SCT is highly prevalent.[12] This concomitant presence of T2DM and SCT in sub-Saharan region is bound to give warning call to the health authorities.
  11 in total

Review 1.  Sickle-cell disease.

Authors:  Marie J Stuart; Ronald L Nagel
Journal:  Lancet       Date:  2004 Oct 9-15       Impact factor: 79.321

Review 2.  The natural history of sickle cell disease.

Authors:  Graham R Serjeant
Journal:  Cold Spring Harb Perspect Med       Date:  2013-10-01       Impact factor: 6.915

Review 3.  Sickle-cell disease.

Authors:  G R Serjeant
Journal:  Lancet       Date:  1997-09-06       Impact factor: 79.321

Review 4.  Obesity and type 2 diabetes in Sub-Sahara Africa.

Authors:  Jean Claude Mbanya; Felix K Assah; Jude Saji; Emmanuella N Atanga
Journal:  Curr Diab Rep       Date:  2014-07       Impact factor: 4.810

Review 5.  Oxidative stress in sickle cell disease; pathophysiology and potential implications for disease management.

Authors:  Erfan Nur; Bart J Biemond; Hans-Martin Otten; Dees P Brandjes; John-John B Schnog
Journal:  Am J Hematol       Date:  2011-05-04       Impact factor: 10.047

6.  Relationship between oxidative stress, ferritin and insulin resistance in sickle cell disease.

Authors:  A I Alsultan; M A Seif; T T Amin; M Naboli; A M Alsuliman
Journal:  Eur Rev Med Pharmacol Sci       Date:  2010-06       Impact factor: 3.507

Review 7.  The role of oxidative stress in hemolytic anemia.

Authors:  Eitan Fibach; Eliezer Rachmilewitz
Journal:  Curr Mol Med       Date:  2008-11       Impact factor: 2.222

8.  Sickle-cell anaemia: an explanation for the ancient myth of reincarnation in Nigeria.

Authors:  J K Onwubalili
Journal:  Lancet       Date:  1983-08-27       Impact factor: 79.321

9.  The effect of oxidative stress on human red cells glutathione peroxidase, glutathione reductase level, and prevalence of anemia among diabetics.

Authors:  Hisham Waggiallah; Mohammed Alzohairy
Journal:  N Am J Med Sci       Date:  2011-07

10.  Sickle Cell Trait Worsens Oxidative Stress, Abnormal Blood Rheology, and Vascular Dysfunction in Type 2 Diabetes.

Authors:  Mor Diaw; Vincent Pialoux; Cyril Martin; Abdoulaye Samb; Saliou Diop; Camille Faes; Pauline Mury; Niama Sall Diop; Saïd-Norou Diop; Brigitte Ranque; Maïmouna Ndour Mbaye; Nigel S Key; Philippe Connes
Journal:  Diabetes Care       Date:  2015-08-31       Impact factor: 19.112

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