A rare case of renal angiomyolipoma involved both inferior vena cava and pulmonary arteries.

Angiomyolipoma is a benign mesenchymal tumour, which rarely involve inferior vena cava (IVC) and pulmonary arteries. Here we reported a 41-year-old man, who presented symptoms of chronic pulmonary embolism. After multiple images evaluation, a large tumour with the same properties as the pulmonary embolism was found in the right kidney. One-staged surgery to remove both pulmonary embolism and right kidney was performed. Histological study showed the tumour and embolism as angiomyolipoma. The present study reported a rare case with renal angiomyolipoma and both IVC and pulmonary arteries involvements, which provided a good example for differential diagnosis in the emergency department and treating a rare type of chronic pulmonary embolism after renal angiomyolipoma.