Literature DB >> 29679356

Regional variations in immunosuppressive therapy in patients with primary nephrotic syndrome: the Japan nephrotic syndrome cohort study.

Ryohei Yamamoto1, Enyu Imai2, Shoichi Maruyama3, Hitoshi Yokoyama4, Hitoshi Sugiyama5, Kosaku Nitta6, Tatsuo Tsukamoto7, Shunya Uchida8, Asami Takeda9, Toshinobu Sato10, Takashi Wada11, Hiroki Hayashi12, Yasuhiro Akai13, Megumu Fukunaga14, Kazuhiko Tsuruya15, Kosuke Masutani16, Tsuneo Konta17, Tatsuya Shoji18, Takeyuki Hiramatsu19, Shunsuke Goto20, Hirofumi Tamai21, Saori Nishio22, Arimasa Shirasaki23, Kojiro Nagai24, Kunihiro Yamagata25, Hajime Hasegawa26, Hidemo Yasuda27, Shizunori Ichida28, Tomohiko Naruse29, Kei Fukami30, Tomoya Nishino31, Hiroshi Sobajima32, Satoshi Tanaka33, Toshiyuki Akahori34, Takafumi Ito35, Terada Yoshio36, Ritsuko Katafuchi37, Shouichi Fujimoto38, Hirokazu Okada39, Eiji Ishimura40, Junichiro James Kazama41, Keiju Hiromura42, Tetsushi Mimura43, Satashi Suzuki44, Yosuke Saka45, Tadashi Sofue46, Yusuke Suzuki47, Yugo Shibagaki48, Kiyoki Kitagawa49, Kunio Morozumi50, Yoshiro Fujita51, Makoto Mizutani52, Takashi Shigematsu53, Naoki Kashihara54, Hiroshi Sato55, Seiichi Matsuo3, Ichiei Narita56, Yoshitaka Isaka57.   

Abstract

BACKGROUND: The lack of high-quality clinical evidences hindered broad consensus on optimal therapies for primary nephrotic syndromes. The aim of the present study was to compare prevalence of immunosuppressive drug use in patients with primary nephrotic syndrome across 6 regions in Japan.
METHODS: Between 2009 and 2010, 380 patients with primary nephrotic syndrome in 56 hospitals were enrolled in a prospective cohort study [Japan Nephrotic Syndrome Cohort Study (JNSCS)], including 141, 151, and 38 adult patients with minimal change disease (MCD), membranous nephropathy (MN), and focal segmental glomerulosclerosis (FSGS), respectively. Their clinical characteristics were compared with those of patients registered in a large nationwide registry of kidney biopsies [Japan Renal Biopsy Registry (J-RBR)]. The regional prevalence of use of each immunosuppressive drug was assessed among adult MCD, MN, and FSGS patients who underwent immunosuppressive therapy in the JNSCS (n = 139, 127, and 34, respectively). Predictors of its use were identified using multivariable-adjusted logistic regression models.
RESULTS: The clinical characteristics of JNSCS patients were comparable to those of J-RBR patients, suggesting that the JNSCS included the representatives in the J-RBR. The secondary major immunosuppressive drugs were intravenous methylprednisolone [n = 33 (24.6%), 24 (19.7%), and 9 (28.1%) in MCD, MN, and FSGS, respectively] and cyclosporine [n = 25 (18.7%), 62 (50.8%), and 16 (50.0%), respectively]. The region was identified as a significant predictor of use of intravenous methylprednisolone in MCD and MN patients.
CONCLUSION: Use of intravenous methylprednisolone for MCD and MN differed geographically in Japan. Its efficacy should be further evaluated in a well-designed trial.

Entities:  

Keywords:  Cyclosporine; Focal and segmental glomerulosclerosis; Membranous nephropathy; Methylprednisolone; Minimal change disease

Mesh:

Substances:

Year:  2018        PMID: 29679356     DOI: 10.1007/s10157-018-1579-x

Source DB:  PubMed          Journal:  Clin Exp Nephrol        ISSN: 1342-1751            Impact factor:   2.801


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