Literature DB >> 29660409

Chronic intestinal pseudo-obstruction syndrome and gastrointestinal malrotation in an infantwith schaaf-yang syndrome - Expanding the phenotypic spectrum.

Allan Bayat1, Michael Bayat2, Ricardo Lozoya3, Christian P Schaaf3.   

Abstract

We report a novel patient with the phenotypic characteristics of Schaaf-Yang syndrome. In addition, the patient has a severe chronic digestive malfunction, rendering him dependent on intermittent enteral supplementation. To our knowledge, this is the first report of Schaaf-Yang syndrome associated with severe chronic digestive malfunction manifesting with both a malrotation and signs of a chronic intestinal pseudo-obstruction.
Copyright © 2018 Elsevier Masson SAS. All rights reserved.

Entities:  

Keywords:  Chronic digestive malfunction; Chronic intestinal pseudo-obstruction syndrome; MAGEL2; Malrotation; Schaaf-yang syndrome

Mesh:

Substances:

Year:  2018        PMID: 29660409     DOI: 10.1016/j.ejmg.2018.04.007

Source DB:  PubMed          Journal:  Eur J Med Genet        ISSN: 1769-7212            Impact factor:   2.708


  4 in total

1.  A Recurrent Variant in MAGEL2 in Five Siblings with Severe Respiratory Disturbance after Birth.

Authors:  Bing Xiao; Xing Ji; Wei Wei; Yan Hui; Yu Sun
Journal:  Mol Syndromol       Date:  2019-07-05

2.  MAGEL2-related disorders: A study and case series.

Authors:  Jameson Patak; James Gilfert; Melissa Byler; Vamsee Neerukonda; Isabelle Thiffault; Laura Cross; Shivarajan Amudhavalli; Marta Pacio-Miguez; Maria Palomares-Bralo; Sixto Garcia-Minaur; Fernando Santos-Simarro; Zoe Powis; Wendy Alcaraz; Sha Tang; Julie Jurgens; Brenda Barry; Eleina England; Elizabeth Engle; Jonathon Hess; Robert R Lebel
Journal:  Clin Genet       Date:  2019-08-22       Impact factor: 4.438

3.  Diagnosis of Schaaf-Yang syndrome in Korean children with developmental delay and hypotonia.

Authors:  Hyunji Ahn; Go Hun Seo; Arum Oh; Yena Lee; Changwon Keum; Sun Hee Heo; Taeho Kim; Jeongmin Choi; Gu-Hwan Kim; Tae-Sung Ko; Mi-Sun Yum; Beom Hee Lee; In Hee Choi
Journal:  Medicine (Baltimore)       Date:  2020-12-18       Impact factor: 1.817

4.  Schaaf-Yang syndrome overview: Report of 78 individuals.

Authors:  John McCarthy; Philip J Lupo; Erin Kovar; Megan Rech; Bret Bostwick; Daryl Scott; Katerina Kraft; Tony Roscioli; Joel Charrow; Samantha A Schrier Vergano; Edward Lose; Robert Smiegel; Yves Lacassie; Christian P Schaaf
Journal:  Am J Med Genet A       Date:  2018-10-10       Impact factor: 2.802

  4 in total

北京卡尤迪生物科技股份有限公司 © 2022-2023.