Literature DB >> 29654655

Biliary drainage as treatment for allograft steatosis following liver transplantation for PFIC-1 disease: A single-center experience.

Leina S Alrabadi1, Raffaella A Morotti2, Pamela L Valentino1, Manuel I Rodriguez-Davalos3, Udeme D Ekong1, Sukru H Emre3.   

Abstract

Development of macrovesicular steatosis post-LT in patients with PFIC-1 is increasingly being observed, with the etiology not fully understood. We highlight successful and effective EBD for reversal of allograft steatosis in 2 patients with PFIC-1 disease and discuss our experience with internal biliary diversion in this patient population.
© 2018 John Wiley & Sons A/S. Published by John Wiley & Sons Ltd.

Entities:  

Keywords:  zzm321990ATP8B1zzm321990; cholestasis; diarrhea; disease recurrence; graft dysfunction; jaundice

Mesh：

Year:  2018        PMID： 29654655     DOI： 10.1111/petr.13184

Source DB:  PubMed          Journal:  Pediatr Transplant        ISSN： 1397-3142


  6 in total

1.  Ileal Bile Acid Transporter Inhibition Reduces Post-Transplant Diarrhea and Growth Failure in FIC1 Disease-A Case Report.

Authors:  Johanna Ohlendorf; Imeke Goldschmidt; Norman Junge; Tobias Laue; Hamoud Nasser; Elmar Jäckel; Frauke Mutschler; Eva-Doreen Pfister; Diran Herebian; Verena Keitel; Ulrich Baumann
Journal:  Children (Basel)       Date:  2022-05-05

2.  Total Internal Biliary Diversion for Post-Liver Transplant PFIC-1-Related Allograft Injury.

Authors:  Naresh Shanmugam; Jagadeesh Menon; Mukul Vij; Ashwin Rammohan; Rajesh Rajalingam; Mohamed Rela
Journal:  J Clin Exp Hepatol       Date:  2021-03-30

3.  A Report of 2 Infant Siblings with Progressive Intrahepatic Familial Cholestasis Type 1 and a Novel Homozygous Mutation in the ATP8B1 Gene Treated with Partial External Biliary Diversion and Liver Transplant.

Authors:  Irena Jankowska; Joanna Pawłowska; Marek Szymczak; Hor Ismail; Dorota Broniszczak; Joanna Cielecka-Kuszyk; Piotr Socha; Dorota Jarzębicka; Piotr Czubkowski
Journal:  Am J Case Rep       Date:  2021-07-20

4.  Changes in plasma bile acid profiles after partial internal biliary diversion in PFIC2 patients.

Authors:  Teng Liu; Ren-Xue Wang; Jun Han; Yi-Ling Qiu; Christoph H Borchers; Victor Ling; Jian-She Wang
Journal:  Ann Transl Med       Date:  2020-03

Review 5.  Recent updates on progressive familial intrahepatic cholestasis types 1, 2 and 3: Outcome and therapeutic strategies.

Authors:  Seema Alam; Bikrant Bihari Lal
Journal:  World J Hepatol       Date:  2022-01-27

6.  Long-Term Results of Pediatric Liver Transplantation for Progressive Familial Intrahepatic Cholestasis.

Authors:  Chenyue Hang; Yijie Jin; Yi Luo; Mingxuan Feng; Tao Zhou; Jianjun Zhu; Jianjun Zhang; Yuan Liu; Qiang Xia
Journal:  J Clin Med       Date:  2022-08-11       Impact factor: 4.964
  6 in total

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