Literature DB >> 29607204

Incidental adult polysplenia with situs inversus, interrupted inferior vena cava with azygos continuation, patent ductus arteriosus, and aortic branches variations: a case report.

Se Hwan Kwon1, So Youn Shin1.   

Abstract

Polysplenia syndrome is a rare condition (about 2.5:100,000 live births) wherein a person has two or more spleens with accompanying various thoracic and abdominal organ abnormalities. Polysplenia is usually associated with situs ambiguous, while polysplenia with situs inversus is very rare. Herein, we report a rare case of incidentally found polysplenia syndrome combined with situs inversus in a 59-year-old female who also had an interrupted inferior vena cava (IVC) with azygos continuation, patent ductus arteriosus (PDA), and variations in the aortic arch branches. An aberrant left subclavian artery with Kommerell's diverticulum and a large aneurysm in the non-aberrant, proximal-right subclavian artery were also noted.

Entities:  

Keywords:  Polysplenia syndrome; dextrocardia; inferior; situs inversus; splenic diseases; vena cava

Year:  2018        PMID: 29607204      PMCID: PMC5864679          DOI: 10.21037/jtd.2018.01.128

Source DB:  PubMed          Journal:  J Thorac Dis        ISSN: 2072-1439            Impact factor:   2.895


  9 in total

1.  Polysplenia syndrome accompanied with situs inversus totalis and annular pancreas in an elderly patient.

Authors:  Arda Kayhan; Hatice Lakadamyali; Jacob Oommen; Aytekin Oto
Journal:  Clin Imaging       Date:  2010 Nov-Dec       Impact factor: 1.605

2.  Azygos continuation of interrupted inferior vena cava in association with sick sinus syndrome.

Authors:  R Vijayvergiya; M N Bhat; R M Kumar; S G Vivekanand; A Grover
Journal:  Heart       Date:  2005-04       Impact factor: 5.994

Review 3.  The nomenclature, definition and classification of cardiac structures in the setting of heterotaxy.

Authors:  Jeffrey P Jacobs; Robert H Anderson; Paul M Weinberg; Henry L Walters; Christo I Tchervenkov; Danny Del Duca; Rodney C G Franklin; Vera D Aiello; Marie J Béland; Steven D Colan; J William Gaynor; Otto N Krogmann; Hiromi Kurosawa; Bohdan Maruszewski; Giovanni Stellin; Martin J Elliott
Journal:  Cardiol Young       Date:  2007-09       Impact factor: 1.093

4.  Anatomy and radiology of the variations of aortic arch branches in 1,266 patients.

Authors:  G Vučurević; S Marinković; L Puškaš; I Kovačević; S Tanasković; D Radak; A Ilić
Journal:  Folia Morphol (Warsz)       Date:  2013-05       Impact factor: 1.183

5.  Aberrant subclavian artery and Kommerell aneurysm: surgical treatment with a standard approach.

Authors:  Nicholas T Kouchoukos; Paolo Masetti
Journal:  J Thorac Cardiovasc Surg       Date:  2007-04       Impact factor: 5.209

Review 6.  Polysplenia syndrome detected in adulthood: report of eight cases and review of the literature.

Authors:  G Gayer; S Apter; T Jonas; M Amitai; R Zissin; T Sella; P Weiss; M Hertz
Journal:  Abdom Imaging       Date:  1999 Mar-Apr

7.  Isolated levocardia associated with absence of inferior vena cava, lobulated spleen and sick sinus syndrome. A case report.

Authors:  H Kakura; K Miyahara; H Sohara; S Amitani; M Koga; Y Moriyama; A Taira
Journal:  Jpn Heart J       Date:  1998-03

8.  Heterotaxy syndrome.

Authors:  Soo-Jin Kim
Journal:  Korean Circ J       Date:  2011-05-31       Impact factor: 3.243

9.  Polysplenia syndrome associated with situs inversus abdominus and type I jejunal atresia.

Authors:  Farooq Rasool; Bilal Mirza
Journal:  APSP J Case Rep       Date:  2011-07-30
  9 in total
  1 in total

Review 1.  Situs Inversus Totalis: A Clinical Review.

Authors:  Katalin Eitler; András Bibok; Gábor Telkes
Journal:  Int J Gen Med       Date:  2022-03-03
  1 in total

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