| Literature DB >> 29607204 |
Abstract
Polysplenia syndrome is a rare condition (about 2.5:100,000 live births) wherein a person has two or more spleens with accompanying various thoracic and abdominal organ abnormalities. Polysplenia is usually associated with situs ambiguous, while polysplenia with situs inversus is very rare. Herein, we report a rare case of incidentally found polysplenia syndrome combined with situs inversus in a 59-year-old female who also had an interrupted inferior vena cava (IVC) with azygos continuation, patent ductus arteriosus (PDA), and variations in the aortic arch branches. An aberrant left subclavian artery with Kommerell's diverticulum and a large aneurysm in the non-aberrant, proximal-right subclavian artery were also noted.Entities:
Keywords: Polysplenia syndrome; dextrocardia; inferior; situs inversus; splenic diseases; vena cava
Year: 2018 PMID: 29607204 PMCID: PMC5864679 DOI: 10.21037/jtd.2018.01.128
Source DB: PubMed Journal: J Thorac Dis ISSN: 2072-1439 Impact factor: 2.895