Literature DB >> 29594173

Acinar Cell Cystadenoma - a Rarity in Advanced von Hippel-Lindau Disease: A Case Report.

Tim Fahlbusch1, Andrea Tannapfel2, Waldemar Uhl1, Chris Braumann1.   

Abstract

BACKGROUND: Von Hippel-Lindau (VHL) disease may occur at various localisations which can be both intra- and extrapancreatic as well as challenging to diagnose by medical imaging. CASE REPORT: A positron emission tomography/magnetic resonance imaging in a 40-year-old woman was performed to monitor a haemangioblastoma. Additionally, it showed findings which were considered to be a pancreatic neuroendocrine tumour (pNET) and retroumbilical metastasis. The suspected metastasis was laparoscopically resected; however, pathological evaluation did not lead to a clear categorisation. Consequently, the pancreatic head was resected in which a pNET and various acinar cell cystadenomas were found.
CONCLUSION: Diagnostic and therapy of advanced VHL disease can be difficult; if in doubt, a surgical approach may establish clarity.

Entities:  

Keywords:  Acinar cell cystadenoma; Pancreatic neuroendocrine tumour, pNET; von Hippel-Lindau disease

Year:  2017        PMID： 29594173      PMCID： PMC5869601          DOI： 10.1159/000480372

Source DB:  PubMed          Journal:  Visc Med        ISSN： 2297-4725


  11 in total

1.  ENETS Consensus Guidelines Update for the Management of Distant Metastatic Disease of Intestinal, Pancreatic, Bronchial Neuroendocrine Neoplasms (NEN) and NEN of Unknown Primary Site.

Authors:  M Pavel; D O'Toole; F Costa; J Capdevila; D Gross; R Kianmanesh; E Krenning; U Knigge; R Salazar; U-F Pape; K Öberg
Journal:  Neuroendocrinology       Date:  2016-01-05       Impact factor: 4.914

2.  von Hippel-Lindau disease-associated solid microcystic serous adenomas masquerading as pancreatic neuroendocrine neoplasms.

Authors:  Simon Turcotte; Baris Turkbey; Stephanie Barak; Steven K Libutti; H Richard Alexander; W Marston Linehan; Marybeth S Hughes; Naris Nilubol; Krisana Gesuwan; Corina Millo; Martha Quezado; Peter L Choyke; Electron Kebebew; Giao Q Phan
Journal:  Surgery       Date:  2012-10-27       Impact factor: 3.982

Review 3.  Pancreatic lesions in von Hippel-Lindau disease? A systematic review and meta-synthesis of the literature.

Authors:  Michael Charlesworth; Caroline S Verbeke; Gavin A Falk; Matthew Walsh; Andrew M Smith; Gareth Morris-Stiff
Journal:  J Gastrointest Surg       Date:  2012-02-28       Impact factor: 3.452

4.  Survival and causes of death in patients with von Hippel-Lindau disease.

Authors:  Marie Louise Mølgaard Binderup; Annette Møller Jensen; Esben Budtz-Jørgensen; Marie Luise Bisgaard
Journal:  J Med Genet       Date:  2016-08-18       Impact factor: 6.318

Review 5.  Pancreatic involvement in von Hippel-Lindau disease: report of two cases and review of the literature.

Authors:  Luca Elli; Elisabetta Buscarini; Vanessa Portugalli; Luigi Reduzzi; Chiara Reduzzi; Gianfranco Brambilla; Fernanda Menozzi; Maria Teresa Bardella; Luca P Piodi; Maja Caldato; Alessandro Zambelli
Journal:  Am J Gastroenterol       Date:  2006-09-04       Impact factor: 10.864

6.  Abdominal visceral lesions in von Hippel-Lindau disease: incidence and clinical behavior of pancreatic and adrenal lesions at a single center.

Authors:  Keith A Delman; Suzanne E Shapiro; Eric W Jonasch; Jeffrey E Lee; Steven A Curley; Douglas B Evans; Nancy D Perrier
Journal:  World J Surg       Date:  2006-05       Impact factor: 3.352

7.  ENETS Consensus Guidelines Update for the Management of Patients with Functional Pancreatic Neuroendocrine Tumors and Non-Functional Pancreatic Neuroendocrine Tumors.

Authors:  M Falconi; B Eriksson; G Kaltsas; D K Bartsch; J Capdevila; M Caplin; B Kos-Kudla; D Kwekkeboom; G Rindi; G Klöppel; N Reed; R Kianmanesh; R T Jensen
Journal:  Neuroendocrinology       Date:  2016-01-05       Impact factor: 4.914

8.  Pancreatic neuroendocrine tumors associated with von Hippel Lindau disease: diagnostic and management recommendations.

Authors:  S K Libutti; P L Choyke; D L Bartlett; H Vargas; M Walther; I Lubensky; G Glenn; W M Linehan; H R Alexander
Journal:  Surgery       Date:  1998-12       Impact factor: 3.982

Review 9.  Pancreatic cysts: pathologic classification, differential diagnosis, and clinical implications.

Authors:  Olca Basturk; Ipek Coban; N Volkan Adsay
Journal:  Arch Pathol Lab Med       Date:  2009-03       Impact factor: 5.534

Review 10.  von Hippel-Lindau disease.

Authors:  Russell R Lonser; Gladys M Glenn; McClellan Walther; Emily Y Chew; Steven K Libutti; W Marston Linehan; Edward H Oldfield
Journal:  Lancet       Date:  2003-06-14       Impact factor: 79.321
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