Literature DB >> 29404153

Quality of Life Questionnaire for Turkish Patients with Primary Ciliary Dyskinesia.

Nagehan Emiralioğlu1, Bülent Karadağ2, H Uğur Özçelik1.   

Abstract

OBJECTIVES: Primary ciliary dyskinesia (PCD) is a major cause of progressive lung disease, and physiological measures do not reflect the impact of the disease on patients' daily symptoms or physical and social functions. We need valid and reliable health-related quality-of-life (HRQOL) measures in PCD to assess the symptoms and daily functions from the patient's perspective. Our aim was to develop a Turkish translation of PCD-specific HRQOL questionnairre to be used as outcomes in clinical trials.
MATERIAL AND METHODS: This study was conducted at the Division of Pediatric Pulmonology, Hacettepe University Faculty of Medicine and the Division of Pediatric Pulmonology, Marmara University Faculty of Medicine. Forward and back translations were performed by three different translators. We recruited participants with PCD from different age groups of both sexes, with an aim to represent a wide spectrum of disease severity and performed the prototype of the translation in these participants.
RESULTS: Five participants from each age group [children (6-12 years), teenagers (13-17 years), adults (18+ years) and parents of children aged from 6 to 12 years] responded to the HRQOL questionnaire. Content analysis of the questions included the following domains depending on age: Respiratory Symptoms, Physical Functioning, Emotional Functioning, Treatment Burden, Ears and Hearing, Sinus Symptoms, Social Functioning, Role Functioning, Vitality, Health Perceptions, School Functioning, Eating and Weight. After the participants have completed the questionnaire, a cognitive debriefing interview was conducted with them, and the results of the interviews were used to form a final version of PCD-specific HRQOL, ready for formal validation.
CONCLUSION: A Turkish translation of PCD-specific HRQOL questionnaire was developed to meet the standards set by international guidelines. This questionnaire is expected to be useful as end points in clinical trials for monitoring health outcomes and for improving clinical decisions.

Entities:  

Keywords:  Primary ciliary dyskinesia; forward translation; quality of life questionnaire

Year:  2017        PMID: 29404153      PMCID: PMC5783167          DOI: 10.5152/TurkThoracJ.2017.16049

Source DB:  PubMed          Journal:  Turk Thorac J        ISSN: 2148-7197


  17 in total

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Authors:  Mieke Boon; Mark Jorissen; Marijke Proesmans; Kris De Boeck
Journal:  Eur J Pediatr       Date:  2012-07-10       Impact factor: 3.183

2.  Progression of lung disease in primary ciliary dyskinesia: is spirometry less accurate than CT?

Authors:  Marco Maglione; Andrew Bush; Silvia Montella; Carmine Mollica; Angelo Manna; Antonietta Esposito; Francesca Santamaria
Journal:  Pediatr Pulmonol       Date:  2011-10-17

3.  Psychometric evaluation of the Cystic Fibrosis Questionnaire-Revised in a national sample.

Authors:  Alexandra L Quittner; Gregory S Sawicki; Ann McMullen; Lawrence Rasouliyan; David J Pasta; Ashley Yegin; Michael W Konstan
Journal:  Qual Life Res       Date:  2011-10-14       Impact factor: 4.147

4.  Quality of Life Questionnaire-Bronchiectasis: final psychometric analyses and determination of minimal important difference scores.

Authors:  Alexandra L Quittner; Anne E O'Donnell; Matthias A Salathe; Sandra A Lewis; Xiaoming Li; A Bruce Montgomery; Thomas G O'Riordan; Alan F Barker
Journal:  Thorax       Date:  2014-10-16       Impact factor: 9.139

Review 5.  Primary Ciliary Dyskinesia: An Update on New Diagnostic Modalities and Review of the Literature.

Authors:  Rizwana Popatia; Kenan Haver; Alicia Casey
Journal:  Pediatr Allergy Immunol Pulmonol       Date:  2014-06-01       Impact factor: 1.349

6.  Lung clearance index and high-resolution computed tomography scores in primary ciliary dyskinesia.

Authors:  Samantha J Irving; Andrew Ives; Gwyneth Davies; Jackie Donovan; Anthony J Edey; Simon S Gill; Arjun Nair; Clare Saunders; Nevin T Wijesekera; Eric W F W Alton; David Hansell; Claire Hogg; Jane C Davies; Andrew Bush
Journal:  Am J Respir Crit Care Med       Date:  2013-09-01       Impact factor: 21.405

Review 7.  Overcoming challenges in the management of primary ciliary dyskinesia: the UK model.

Authors:  Jane S Lucas; Philip Chetcuti; Fiona Copeland; Claire Hogg; Tom Kenny; Eduardo Moya; Christopher O'Callaghan; Woolf T Walker
Journal:  Paediatr Respir Rev       Date:  2013-06-12       Impact factor: 2.726

8.  Health-related quality of life and unmet needs in patients with primary ciliary dyskinesia.

Authors:  M Pifferi; A Bush; M Di Cicco; U Pradal; V Ragazzo; P Macchia; A L Boner
Journal:  Eur Respir J       Date:  2009-09-24       Impact factor: 16.671

9.  A quality-of-life measure for adults with primary ciliary dyskinesia: QOL-PCD.

Authors:  Jane S Lucas; Laura Behan; Audrey Dunn Galvin; Adrianne Alpern; Anjana M Morris; Mary P Carroll; Michael R Knowles; Margaret W Leigh; Alexandra L Quittner
Journal:  Eur Respir J       Date:  2015-05-14       Impact factor: 16.671

10.  Diagnosis and management of primary ciliary dyskinesia.

Authors:  Claudius Werner; Jörg Große Onnebrink; Heymut Omran
Journal:  Cilia       Date:  2015-01-22
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  2 in total

1.  Health related quality of life in adult primary Ciliary dyskinesia patients in Cyprus: development and validation of the Greek version of the QOL-PCD questionnaire.

Authors:  Phivos Ioannou; Panayiotis Kouis; Maria G Kakkoura; Margarita Kaliva; Aristoula Toliopoulou; Kyriacos Andreou; Laura Behan; Jane S Lucas; Vicky Papanikolaou; George Charalambous; Nicos Middleton; Panayiotis K Yiallouros
Journal:  Health Qual Life Outcomes       Date:  2020-04-22       Impact factor: 3.186

Review 2.  Lower airway clinical outcome measures for use in primary ciliary dyskinesia research: a scoping review.

Authors:  Florian Gahleitner; James Thompson; Claire L Jackson; Jana F Hueppe; Laura Behan; Eleonora Dehlink; Myrofora Goutaki; Florian Halbeisen; Ana Paula L Queiroz; Guillaume Thouvenin; Claudia E Kuehni; Philipp Latzin; Jane S Lucas; Bruna Rubbo
Journal:  ERJ Open Res       Date:  2021-11-29
  2 in total

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