Literature DB >> 29396915

P63 expression plays a role in developmental rate, embryo size, and local morphogenesis.

Julia C Boughner1, Matthijs C van Eede2, Shoshana Spring2, Lisa X Yu2, Nasim Rostampour1, R Mark Henkelman2,3.   

Abstract

BACKGROUND: The p63 gene is integral to the development of many body parts including limb, palate, teeth, and urogenital tract. Loss of p63 expression may alter developmental rate, which is crucial to normal morphogenesis. To validate a novel, unbiased embryo phenotyping software tool, we tested whether delayed development contributes to the pathological phenotype of a p63 mouse mutant (p63-/- ). We quantified dysmorphology in p63-/- embryos and tested for universal growth delay relative to wild-type (WT) embryos. Fixed embryos (n = 6; p63-/- ) aged day (E) 15.5 were micro-CT scanned and quantitatively analyzed using a digital WT atlas that defined volumetric differences between p63-/- and WT embryos.
RESULTS: p63-/- embryos showed a growth delay of approximately 22 hr (0.9 days). Among the E15.5 mutants, overall size was closest to WT E14.6 mice but shape was closest to WT E14.0. The atlas clearly identified in p63-/- embryos malformations of epithelial derivatives including limbs, tail, urogenital structures, brain, face, and tooth.
CONCLUSIONS: The software atlas technique described the p63-/- phenotype as a combination of developmental delay (i.e., heterochrony) and malformation (i.e., pathological shape; failed organogenesis). This study identifies for the first time global and local roles for p63 in prenatal growth and development. Developmental Dynamics 247:779-787, 2018.
© 2018 Wiley Periodicals, Inc. © 2018 Wiley Periodicals, Inc.

Entities:  

Keywords:  3D imaging; 4D Atlas; Tp63; Trp63; heterochrony; micro-CT; mouse; organogenesis

Mesh:

Substances:

Year:  2018        PMID: 29396915     DOI: 10.1002/dvdy.24622

Source DB:  PubMed          Journal:  Dev Dyn        ISSN: 1058-8388            Impact factor:   3.780


  5 in total

1.  The venous system of E14.5 mouse embryos-reference data and examples for diagnosing malformations in embryos with gene deletions.

Authors:  Stefan H Geyer; Barbara Maurer-Gesek; Lukas F Reissig; Julia Rose; Fabrice Prin; Robert Wilson; Antonella Galli; Catherine Tudor; Jacqueline K White; Timothy J Mohun; Wolfgang J Weninger
Journal:  J Anat       Date:  2021-08-25       Impact factor: 2.921

Review 2.  p63-related signaling at a glance.

Authors:  Matthew L Fisher; Seamus Balinth; Alea A Mills
Journal:  J Cell Sci       Date:  2020-09-11       Impact factor: 5.285

3.  BRD4 Regulates Transcription Factor ΔNp63α to Drive a Cancer Stem Cell Phenotype in Squamous Cell Carcinomas.

Authors:  Matthew L Fisher; Seamus Balinth; Yon Hwangbo; Caizhi Wu; Carlos Ballon; John E Wilkinson; Gary L Goldberg; Alea A Mills
Journal:  Cancer Res       Date:  2021-10-25       Impact factor: 13.312

4.  An NKX2-1GFP and TP63tdTomato dual fluorescent reporter for the investigation of human lung basal cell biology.

Authors:  Kim Jee Goh; Ee Kim Tan; Hao Lu; Sudipto Roy; N Ray Dunn
Journal:  Sci Rep       Date:  2021-02-25       Impact factor: 4.379

5.  Tooth defects of EEC and AEC syndrome caused by heterozygous TP63 mutations in three Chinese families and genotype-phenotype correlation analyses of TP63-related disorders.

Authors:  Jinglei Zheng; Haochen Liu; Yuan Zhan; Yang Liu; Sing-Wai Wong; Tao Cai; Hailan Feng; Dong Han
Journal:  Mol Genet Genomic Med       Date:  2019-05-02       Impact factor: 2.183

  5 in total

北京卡尤迪生物科技股份有限公司 © 2022-2023.