| Literature DB >> 29325956 |
Michael A Galgano1, Carlos R Goulart2, Karen Chisholm3, Melissa Hazen4, Scellig Stone5.
Abstract
BACKGROUND: Isolated intraspinal neurosarcoidosis is a rare clinical entity, with most reports describing intramedullary involvement in adults. CASE DESCRIPTION: We detail the case of a 9-year-old girl with rapid-onset compressive myelopathy secondary to a thoracic epidural lesion. Although pathologic diagnosis was challenging, a presumptive diagnosis of isolated extradural neurosarcoidosis was made in light of the patient's investigations and dramatic response to corticosteroids.Entities:
Keywords: Inflammatory granulomatous disease; Isolated intraspinal neurosarcoidosis; Neurosarcoidosis; Rheumatology; Spine
Mesh:
Substances:
Year: 2018 PMID: 29325956 DOI: 10.1016/j.wneu.2017.12.185
Source DB: PubMed Journal: World Neurosurg ISSN: 1878-8750 Impact factor: 2.104