Literature DB >> 29302938

Long-Term Results of Aortic Root Surgery in Marfan Syndrome Patients: A Single-Center Experience.

Francesco Nicolo1, Francesco Romeo2, Antonio Lio3, Emanuele Bovio3, Antonio Scafuri3, Carlo Bassano3, Patrizio Polisca3, Antonio Pellegrino3, Paolo Nardi3, Luigi Chiariello4, Giovanni Ruvolo3.   

Abstract

BACKGROUND AND AIM OF THE STUDY: The study aim was to compare long-term results of Marfan syndrome (MFS) patients affected by aortic root disease undergoing aortic root replacement with the Bentall or David operation.
METHODS: Since 1994, a total of 59 patients has been followed at the authors' Marfan Center, having undergone either a Bentall operation (Bentall group, n = 30) or a David operation (David group, n = 29).
RESULTS: No operative mortality was recorded. After 20 years (mean follow up 97 ± 82 months; range 1 to 369 months) no prosthesis-related major bleeding or thromboembolic events had been observed; the 20-year survival was 94 ± 6% in the Bentall group, and 100% in the David group (p = 0.32). Freedom from reintervention for aortic valve dysfunction was 100% in the Bentall group, and 75 ± 13% in the David group (p = 0.04). This inter-group difference became relevant after the first eight-year period of follow-up, and was mainly associated with a particular familiar genetic phenotype involving three out of four reoperated patients. Freedom from all-cause death, myocardial infarction, stroke, prosthetic valve-related complications, and reintervention on any aortic segment was 69 ± 12% in the Bentall group, and 67 ± 14% in the David group (p = 0.33).
CONCLUSIONS: The Bentall and David operations are both associated with satisfactory long-term results in MFS patients. The low rate of valve prosthesis-related complications suggested that the Bentall operation would continue to be a standard surgical treatment. The reimplantation technique, adopted for less-dilated aortas, provides satisfactory freedom from reoperation. Careful attention should be paid to the reimplantation technique in patients affected by a serious familiar genetic phenotype.

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Year:  2017        PMID: 29302938

Source DB:  PubMed          Journal:  J Heart Valve Dis        ISSN: 0966-8519


  5 in total

1.  Long term follow-up of Marfan Syndrome - experience of an adult congenital heart disease centre.

Authors:  João F Reis; Tânia B Mano; Tiago Rito; Luísa M Branco; José Fragata; José D Martins; Rui C Ferreira; Lídia Sousa
Journal:  Am J Cardiovasc Dis       Date:  2022-04-15

2.  Systematic review and meta-analysis of aortic valve-sparing surgery versus replacement surgery in ascending aortic aneurysms and dissection in patients with Marfan syndrome and other genetic connective tissue disorders.

Authors:  Maria Elena Soto; Eric Ochoa-Hein; Javier E Anaya-Ayala; Micaela Ayala-Picazo; Solange Gabriela Koretzky
Journal:  J Thorac Dis       Date:  2021-08       Impact factor: 3.005

Review 3.  Imaging of the Postsurgical Aorta in Marfan Syndrome.

Authors:  Lauren K Groner; Christopher Lau; Richard B Devereux; Daniel B Green
Journal:  Curr Treat Options Cardiovasc Med       Date:  2018-08-27

Review 4.  Redo Aortic Root Operations in Patients with Marfan Syndrome.

Authors:  Vicente Orozco-Sevilla; Richard Whitlock; Ourania Preventza; Kim I de la Cruz; Joseph S Coselli
Journal:  Int J Angiol       Date:  2018-05-17

5.  Decision-making at initial surgery for type A aortic dissection in patients with Marfan syndrome: proximal or extensive repair.

Authors:  Ning Li; Yu Zhang; Yuan Gao; Yifan Bai; Zhao An; Guanxin Zhang; Qingqi Han; Fanglin Lu; BaiLing Li; Lin Han; Zhiyun Xu
Journal:  J Thorac Dis       Date:  2019-12       Impact factor: 2.895

  5 in total

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