| Literature DB >> 29285766 |
Masaru Kato1, Tatsuya Atsumi1.
Abstract
Recent studies have clarified that pulmonary arterial hypertension associated with connective tissue diseases (CTD-PAH) has some distinctive clinical aspects from other PAH, such as high prevalence, venous and cardiac involvement, less favourable outcome, helpfulness of detection algorithm, response to immunosuppression, pre-PAH conditions in borderline pulmonary arterial pressure and coexistence of interstitial lung disease. In this review, by focusing on these distinctive aspects, we discuss how to provide an efficacious and safe management of CTD-PAH and garner attention to areas where further evidence is desired.Entities:
Keywords: connective tissue diseases; pulmonary arterial hypertension; pulmonary hypertension; systemic lupus erythematosus; systemic sclerosis
Mesh:
Substances:
Year: 2017 PMID: 29285766 DOI: 10.1111/eci.12876
Source DB: PubMed Journal: Eur J Clin Invest ISSN: 0014-2972 Impact factor: 4.686