Literature DB >> 29258971

Adult-onset Rasmussen encephalitis associated with focal cortical dysplasia.

Katharina Hohenbichler1, Julie Lelotte2, Renaud Lhommel3, Riëm El Tahry1, Pascal Vrielynck4, Susana Ferrao Santos1.   

Abstract

Rasmussen encephalitis is a rare, devastating condition, typically presenting in childhood. Cases of adult-onset Rasmussen have also been described, but the clinical picture is less defined, rendering final diagnosis difficult. We present a case of adult-onset Rasmussen encephalitis with dual pathology, associated with focal cortical dysplasia and encephalitis. We interpreted the Rasmussen encephalitis to be caused by severe and continuous epileptic activity due to focal cortical dysplasia. The best therapeutic approach for such cases remains unclear.

Entities:  

Keywords:  adult-onset Rasmussen encephalitis; dual pathology; focal cortical dysplasia

Mesh:

Year:  2017        PMID: 29258971     DOI: 10.1684/epd.2017.0947

Source DB:  PubMed          Journal:  Epileptic Disord        ISSN: 1294-9361            Impact factor:   1.819


  1 in total

1.  Adult-onset Rasmussen's Syndrome with associated cortical dysplasia.

Authors:  C Ákos Szabó; Rachel Garvin; Shaheryar Hafeez; Ali Seifi; Linda Leary; Ratna Bhavaraju-Sanka; James M Henry; Alex M Papanastassiou
Journal:  Epilepsy Behav Case Rep       Date:  2018-11-28
  1 in total

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