Literature DB >> 29177016

'Caterpillar right ventricle': unusual manifestation of a rare disease.

Suneesh Kalliath1, Gopalan Nair Rajesh1.   

Abstract

A 66-year-old man presented with abdominal distension and pedal oedema for the past 10 years. He had history of right heart failure on several occasions in the past, and one of these admissions prompted referral to a cardiac specialist. On examination, he had markedly elevated jugular venous pressure with prominent 'y-descent', a tricuspid regurgitation murmur, gross ascites and pedal oedema. A full blood count, routine biochemical screen and serum bicarbonate levels were normal. Right ventricular angiogram revealed a 'caterpillar'-like aneurysm of the right ventricle (RV) apex (figure 1 arrow) with a dilated right ventricular outflow tract and significant tricuspid regurgitation with a dilated right atrium (see online supplementary video 1). Figure 1 Acine angiographic frame of the right ventricle in posteroanterior view, showing a 'caterpillar'-like right ventricle aneurysm (arrow). 10.1136/heartasia-2017-010957.supp3Supplementary file 3. QUESTION: On the basis of the clinical and right ventriculography features, what is the most likely diagnosis for this patient?Arrhythmogenic right ventricular cardiomyopathy (ARVC)Right ventricular endomyocardial fibrosis (RV-EMF) with an RV aneurysmCardiac sarcoidosisCongenital diverticulum of the right ventricle.

Entities:  

Keywords:  arrhythmogenic right ventricular dyplasia; cardiomyopathy apical; cardiomyopathy restrictive

Year:  2017        PMID: 29177016      PMCID: PMC5692100          DOI: 10.1136/heartasia-2017-010957

Source DB:  PubMed          Journal:  Heart Asia        ISSN: 1759-1104


  5 in total

1.  Two-dimensional echocardiographic findings in systemic sarcoidosis.

Authors:  D J Burstow; A J Tajik; K R Bailey; R A DeRemee; C P Taliercio
Journal:  Am J Cardiol       Date:  1989-02-15       Impact factor: 2.778

2.  Congenital diverticula of the right ventricle of the heart: a case report.

Authors:  R Pressoir; J W Downing
Journal:  J Natl Med Assoc       Date:  1980-03       Impact factor: 1.798

3.  A population study of endomyocardial fibrosis in a rural area of Mozambique.

Authors:  Ana Olga Mocumbi; Maria Beatriz Ferreira; Daniel Sidi; Magdi H Yacoub
Journal:  N Engl J Med       Date:  2008-07-03       Impact factor: 91.245

Review 4.  Endomyocardial fibrosis: still a mystery after 60 years.

Authors:  Gene Bukhman; John Ziegler; Eldryd Parry
Journal:  PLoS Negl Trop Dis       Date:  2008-02-27

5.  Endomyocardial fibrosis with right ventricular aneurysm mimicking ARVC - A case report from India.

Authors:  Suneesh Kalliath; Rajesh Gopalan Nair; Haridasan Vellani
Journal:  Indian Heart J       Date:  2016-08-29
  5 in total

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