I Majdoub1, S Kallel2, M Hsairi3, M Snoussi4, M Charfi3, A Ben Halima3, A Frikha3, M Weli3, F Safi3, L Gargouri3, N Ben Halima3, A Mahfoudh3, A Ghorbel2, Z Bahloul4. 1. Service de pédiatrie, urgence et réanimation pédiatriques, CHU Hédi Chaker, 3029 Sfax, Tunisie. Electronic address: majdoub.imen@yahoo.fr. 2. Service d'oto-rhino-larynologie, CHU Habib Bourguiba, route El Ain km 0.5, Sfax, Tunisie. 3. Service de pédiatrie, urgence et réanimation pédiatriques, CHU Hédi Chaker, 3029 Sfax, Tunisie. 4. Service de médecine interne, CHU Hédi Chaker, 3029 Sfax, Tunisie.
Abstract
Sjögren syndrome is uncommon in children and occurs most often in association with autoimmune diseases (secondary Sjögren syndrome). We describe the clinical and biological features of a 7-year-old girl with primary Sjögren syndrome revealed by recurrent parotiditis. CASE REPORT: A 7-year-old girl was referred for investigation of multiple episodes of parotid swelling since age 4 years, without systemic symptoms. The examination was unremarkable except for enlarged and painless parotid glands. Laboratory investigations and labial salivary gland biopsy revealed Sjögren syndrome without associated disease. Hydroxychloroquine was prescribed with clinical improvement. CONCLUSION: Recurrent parotiditis in children is an uncommon condition. The onset of parotid swelling at 5 years or over deserves screening for disimmune disorders, sarcoidosis, or Sjögren syndrome. Diagnosis of Sjögren syndrome is based on diagnostic criteria.
Sjögren syndrome is uncommon in children and occurs most often in association with autoimmune diseases (secondary Sjögren syndrome). We describe the clinical and biological features of a 7-year-old girl with primary Sjögren syndrome revealed by recurrent parotiditis. CASE REPORT: A 7-year-old girl was referred for investigation of multiple episodes of parotid swelling since age 4 years, without systemic symptoms. The examination was unremarkable except for enlarged and painless parotid glands. Laboratory investigations and labial salivary gland biopsy revealed Sjögren syndrome without associated disease. Hydroxychloroquine was prescribed with clinical improvement. CONCLUSION: Recurrent parotiditis in children is an uncommon condition. The onset of parotid swelling at 5 years or over deserves screening for disimmune disorders, sarcoidosis, or Sjögren syndrome. Diagnosis of Sjögren syndrome is based on diagnostic criteria.