Literature DB >> 29126538

Recurrent Pulmonary Aneurysms: Hughes-Stovin Syndrome on the Spectrum of Behçet Disease.

Sami M Bennji1, Leonard du Preez2, Stephanie Griffith-Richards3, Derrick P Smit4, Jonathan Rigby5, Coenraad F N Koegelenberg6, Elvis M Irusen6, Brian W Allwood6.   

Abstract

In this report, we describe a male patient who presented with recurrent life-threatening hemoptysis due to the sequential formation of multiple pulmonary aneurysms. Both pulmonary artery coil embolization and right lower lobectomy were performed, with limited success. The patient experienced extensive bilateral femoral DVT extending into the inferior vena cava, with massive hemoptysis, fulfilling the diagnosis of Hughes-Stovin syndrome. A final diagnosis of Behçet disease was made following extensive investigation, and the patient responded well to prednisone 20 mg orally and azathioprine 100 mg orally.
Copyright © 2017 American College of Chest Physicians. Published by Elsevier Inc. All rights reserved.

Entities:  

Keywords:  Behçet disease; Hughes-Stovin syndrome; pulmonary aneurysm

Mesh:

Substances:

Year:  2017        PMID: 29126538     DOI: 10.1016/j.chest.2017.07.015

Source DB:  PubMed          Journal:  Chest        ISSN: 0012-3692            Impact factor:   9.410


  4 in total

1.  Pattern of pulmonary vasculitis and major vascular involvement in Hughes-Stovin syndrome (HSS): brief report of eight cases.

Authors:  Yasser Emad; Yasser Ragab; Ossama Ibrahim; Ahmed Saad; Johannes J Rasker
Journal:  Clin Rheumatol       Date:  2019-12-18       Impact factor: 2.980

2.  Transcatheter embolotherapy of pulmonary artery aneurysms as emergency treatment of hemoptysis in Behcet patients: experience of a referral center and a review of the literature.

Authors:  Guillaume Voiriot; Antoine Parrot; Martine Antoine; Aude Gibelin; Samuel Haddad; Marie-France Carette; Muriel Fartoukh; Antoine Khalil
Journal:  Intern Emerg Med       Date:  2018-03-07       Impact factor: 3.397

Review 3.  Phenotypes in Behçet's syndrome.

Authors:  Emire Seyahi
Journal:  Intern Emerg Med       Date:  2019-02-11       Impact factor: 3.397

4.  Pulmonary vasculitis in Hughes-Stovin syndrome (HSS): a reference atlas and computed tomography pulmonary angiography guide-a report by the HSS International Study Group.

Authors:  Yasser Emad; Yasser Ragab; Cal Robinson; Sonia Pankl; Pablo Young; Marianna Fabi; Parag Bawaskar; Ossama Ibrahim; Doruk Erkan; Bhupen Barman; Jasna Tekavec-Trkanjec; Balakrishnan Jayakrishnan; Michael Kindermann; Melek Kechida; Aurelien Guffroy; Rafael S Silva; Faten Frikha; Alaa Abou-Zeid; Maged Hassan; Harrison W Farber; Mohamed H Abdelbary; Leticia Tornes; Jason Margolesky; Nashwa El-Shaarawy; Sami Bennji; Manoj Kumar Agarwala; Ahmed Saad; Taoufik Amezyane; Sergio Ghirardo; Vitor Cruz; Bruno Niemeyer; Khalfan Al-Zeedy; Hamdan Al-Jahdali; Natalia Jaramillo; Serkan Demirkan; Issam Kably; Jung Tae Kim; Johannes J Rasker
Journal:  Clin Rheumatol       Date:  2021-09-17       Impact factor: 2.980

  4 in total

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