Literature DB >> 29017927

Eleclazine exhibits enhanced selectivity for long QT syndrome type 3-associated late Na+ current.

Nesrine El-Bizri1, Cheng Xie1, Lynda Liu1, James Limberis1, Michael Krause1, Ryoko Hirakawa1, Steven Nguyen1, Dennis R Tabuena1, Luiz Belardinelli2, Kristopher M Kahlig3.   

Abstract

BACKGROUND: Eleclazine (GS-6615) is a sodium channel blocker designed to improve the selectivity for cardiac late Na+ current (INa) over peak INa.
OBJECTIVES: The goals of this study were to investigate the inhibition of late INa by eleclazine using a sample of long QT syndrome type 3 (LQT3) and overlap LQT3/Brugada syndrome mutant channels; to compare the apparent binding rates for eleclazine with those for other class 1 antiarrhythmic agents; and to investigate the binding site.
METHODS: Wild-type human cardiac voltage-gated sodium channel (hNaV1.5) and 21 previously reported variants were studied using patch clamp recordings from a heterologous expression system.
RESULTS: Eleclazine inhibited anemone toxin II-enhanced late INa from wild-type hNaV1.5 with a drug concentration that causes 50% block of 0.62 ± 0.12 μM (84-fold selectivity over peak INa). The drug concentration that causes 50% block of eleclazine to inhibit the enhanced late INa from LQT3 mutant channels ranged from 0.33 to 1.7 μM. At predicted therapeutic concentrations, eleclazine and ranolazine inhibited peak INa to a similar degree as assessed with 4 overlap LQT3/Brugada syndrome mutations. Eleclazine was found to interact with hNaV1.5 significantly faster than ranolazine and 6 other class 1 antiarrhythmic agents. Engineered mutations (F1760A/Y1767A) located within the local anesthetic binding site decreased the inhibition of late INa and peak INa by eleclazine.
CONCLUSION: At predicted therapeutic concentrations, eleclazine elicits potent inhibition of late INa across a cohort of NaV1.5 mutant channels. These properties are consistent with a class 1b antiarrhythmic agent that associates with unusually rapid binding/unbinding rates.
Copyright © 2017 Heart Rhythm Society. Published by Elsevier Inc. All rights reserved.

Entities:  

Keywords:  Brugada syndrome; Eleclazine; Long QT syndrome; Ranolazine; Sodium channel

Mesh:

Substances:

Year:  2017        PMID: 29017927     DOI: 10.1016/j.hrthm.2017.09.028

Source DB:  PubMed          Journal:  Heart Rhythm        ISSN: 1547-5271            Impact factor:   6.343


  4 in total

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Journal:  Front Pharmacol       Date:  2020-08-04       Impact factor: 5.810

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Authors:  Hongwei Cheng; Ian Charles; Andrew F James; Ana P Abdala; Jules C Hancox
Journal:  Physiol Rep       Date:  2022-10

4.  Inhibition of voltage-gated Na+ currents by eleclazine in rat atrial and ventricular myocytes.

Authors:  Rachel E Caves; Alexander Carpenter; Stéphanie C Choisy; Ben Clennell; Hongwei Cheng; Cameron McNiff; Brendan Mann; James T Milnes; Jules C Hancox; Andrew F James
Journal:  Heart Rhythm O2       Date:  2020-08
  4 in total

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