Literature DB >> 28986020

Meconium ileus in Cystic Fibrosis.

Meghana Sathe1, Roderick Houwen2.   

Abstract

Meconium ileus (MI) is often the first manifestation of cystic fibrosis (CF) and occurs in approximately 20% of patients diagnosed with CF. This article reviews the pathophysiology of MI and its clinical presentation. It focuses on the medical and surgical management emphasizing the importance of nutrition and a multidisciplinary approach to improve both short-term and long-term outcomes for CF patients with MI.
Copyright © 2017 European Cystic Fibrosis Society. Published by Elsevier B.V. All rights reserved.

Entities:  

Keywords:  Cystic fibrosis; Gastrografin; Meconium ileus; Meconium peritonitis

Mesh：

Year:  2017        PMID： 28986020     DOI： 10.1016/j.jcf.2017.06.007

Source DB:  PubMed          Journal:  J Cyst Fibros        ISSN： 1569-1993            Impact factor:   5.482


  17 in total

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2.  In utero and postnatal VX-770 administration rescues multiorgan disease in a ferret model of cystic fibrosis.

Authors:  Xingshen Sun; Yaling Yi; Ziying Yan; Bradley H Rosen; Bo Liang; Michael C Winter; T Idil Apak Evans; Pavana G Rotti; Yu Yang; Jaimie S Gray; Soo Yeun Park; Weihong Zhou; Yulong Zhang; Shashanna R Moll; Lisa Woody; Dao M Tran; Licong Jiang; Annelotte M Vonk; Jeffrey M Beekman; Paul Negulescu; Fred Van Goor; Dennis F Fiorino; Katherine N Gibson-Corley; John F Engelhardt
Journal:  Sci Transl Med       Date:  2019-03-27       Impact factor: 17.956

3.  Cystic fibrosis and the gut.

Authors:  Mordechai Slae; Michael Wilschanski
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Authors:  Melania Giorgetti; Nikolai Klymiuk; Andrea Bähr; Martin Hemmerling; Lisa Jinton; Robert Tarran; Anna Malmgren; Annika Åstrand; Gunnar C Hansson; Anna Ermund
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6.  Abdominal Surgical Procedures in Adult Patients With Cystic Fibrosis: What Are the Risks?

Authors:  Melissa A Hite; Wolfgang B Gaertner; Bryan Garcia; Patrick A Flume; Pinckney J Maxwell; Virgilio V George; Thomas Curran
Journal:  Dis Colon Rectum       Date:  2022-07-05       Impact factor: 4.412

Review 7.  Progress in Model Systems of Cystic Fibrosis Mucosal Inflammation to Understand Aberrant Neutrophil Activity.

Authors:  Daniel R Laucirica; Luke W Garratt; Anthony Kicic
Journal:  Front Immunol       Date:  2020-04-07       Impact factor: 7.561

Review 8.  Choline in cystic fibrosis: relations to pancreas insufficiency, enterohepatic cycle, PEMT and intestinal microbiota.

Authors:  Wolfgang Bernhard
Journal:  Eur J Nutr       Date:  2020-08-14       Impact factor: 5.614

Review 9.  A new era for people with cystic fibrosis.

Authors:  Marlou C Bierlaagh; Danya Muilwijk; Jeffrey M Beekman; Cornelis K van der Ent
Journal:  Eur J Pediatr       Date:  2021-07-02       Impact factor: 3.183

10.  A comparative study between Santulli ileostomy and loop ileostomy in neonates with meconium ileus.

Authors:  Shahnam Askarpour; Amin Ayatipour; Mehran Peyvasteh; Hazhir Javaherizadeh
Journal:  Arq Bras Cir Dig       Date:  2020-11-13
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