Literature DB >> 28969254

Unusual Clinical Presentations in Early-Onset Childhood Sarcoidosis: A Correlation or Coincidence?

Priyadarshini Sahu1, Sudhanshu Sharma2, Nidhi Sharma3, Sarika Sharma4, Shilpa Garg5.   

Abstract

Sarcoidosis is a multisystem granulomatous disease which frequently affects young adults. Because of its rarity, the exact incidence and prevalence of childhood sarcoidosis is not known. It mostly affects children of older age group i.e., 13-15 years. Early onset sarcoidosis (<5 years) is characterized by a triad of arthritis, uveitis and rash. Late onset sarcoidosis present with a multisystem disease similar to adults, with frequent pulmonary infiltrations and lymphadenopathy. Herein, we report a case of early-onset childhood sarcoidosis in a four-year-old female along with uncommon clinical features like cutaneous ulceration, onycholysis and geographical tongue and its rarity in the literature.

Entities:  

Keywords:  Cutaneous ulceration; Early onset childhood sarcoidosis; Geographical tongue; Onycholysis

Year:  2017        PMID: 28969254      PMCID: PMC5620895          DOI: 10.7860/JCDR/2017/27841.10389

Source DB:  PubMed          Journal:  J Clin Diagn Res        ISSN: 0973-709X


  6 in total

Review 1.  Ulcerative sarcoidosis. Case report and review of the literature.

Authors:  J G Albertini; W Tyler; O F Miller
Journal:  Arch Dermatol       Date:  1997-02

2.  Oral involvement in sarcoidosis: report of 12 cases.

Authors:  A Bouaziz; J Le Scanff; C Chapelon-Abric; L Varron; S Khenifer; A Gleizal; M-H Bentz; A Barthel; D Valeyre; P Seve
Journal:  QJM       Date:  2012-03-14

Review 3.  Evidence-based therapy for cutaneous sarcoidosis.

Authors:  Christy B Doherty; Ted Rosen
Journal:  Drugs       Date:  2008       Impact factor: 9.546

4.  Clinicopathologic features of ulcerative-atrophic sarcoidosis.

Authors:  Simon S Yoo; Daniel Mimouni; Olga V Nikolskaia; David J Kouba; Daniel N Sauder; Carlos H Nousari
Journal:  Int J Dermatol       Date:  2004-02       Impact factor: 2.736

5.  Childhood sarcoidosis in Denmark 1979-1994: incidence, clinical features and laboratory results at presentation in 48 children.

Authors:  A L Hoffmann; N Milman; K E Byg
Journal:  Acta Paediatr       Date:  2004-01       Impact factor: 2.299

6.  Childhood sarcoidosis: A rare but fascinating disorder.

Authors:  Avinash K Shetty; Abraham Gedalia
Journal:  Pediatr Rheumatol Online J       Date:  2008-09-23       Impact factor: 3.054

  6 in total

北京卡尤迪生物科技股份有限公司 © 2022-2023.