| Literature DB >> 28969254 |
Priyadarshini Sahu1, Sudhanshu Sharma2, Nidhi Sharma3, Sarika Sharma4, Shilpa Garg5.
Abstract
Sarcoidosis is a multisystem granulomatous disease which frequently affects young adults. Because of its rarity, the exact incidence and prevalence of childhood sarcoidosis is not known. It mostly affects children of older age group i.e., 13-15 years. Early onset sarcoidosis (<5 years) is characterized by a triad of arthritis, uveitis and rash. Late onset sarcoidosis present with a multisystem disease similar to adults, with frequent pulmonary infiltrations and lymphadenopathy. Herein, we report a case of early-onset childhood sarcoidosis in a four-year-old female along with uncommon clinical features like cutaneous ulceration, onycholysis and geographical tongue and its rarity in the literature.Entities:
Keywords: Cutaneous ulceration; Early onset childhood sarcoidosis; Geographical tongue; Onycholysis
Year: 2017 PMID: 28969254 PMCID: PMC5620895 DOI: 10.7860/JCDR/2017/27841.10389
Source DB: PubMed Journal: J Clin Diagn Res ISSN: 0973-709X