Literature DB >> 28969188

Primary Intestinal Lymphangiectasia (Waldmann's Disease) Presenting with Chylous Effusions in a 15-Year-Old.

Vijay Surampalli1, Srinath Ramaswamy1, Deepanjali Surendran2, Chanaveerappa Bammigatti3, Rathinam Palamalai Swaminathan4.   

Abstract

Primary Intestinal Lymphangiectasia (PIL) is a rare disease of unknown aetiology which presents in the paediatric age group with anasarca, diarrhoea, hypoproteinaemia, lymphoedema and chylous effusions. Tuberculosis, filariasis, chest trauma, malignancies and haematological disorders usually contribute to most cases of secondary lymphangiectasia and chylous effusions. We hereby describe a case of PIL presenting with chylous effusions which remained undiagnosed for eight years.

Entities:  

Keywords:  Fluid accumulation; Hypoproteinaemia; Idiopathic; Lymphatic dilatation; Milky lymph

Year:  2017        PMID： 28969188      PMCID： PMC5620829          DOI： 10.7860/JCDR/2017/29055.10522

Source DB:  PubMed          Journal:  J Clin Diagn Res        ISSN： 0973-709X


  10 in total

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Journal:  Gastroenterology       Date:  1961-09       Impact factor: 22.682

2.  Videocapsule endoscopy is useful for the diagnosis of intestinal lymphangiectasia.

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Journal:  Dig Liver Dis       Date:  2006-03-09       Impact factor: 4.088

Review 3.  Chylothorax: aetiology, diagnosis and therapeutic options.

Authors:  Emmet E McGrath; Zoe Blades; Paul B Anderson
Journal:  Respir Med       Date:  2009-09-18       Impact factor: 3.415

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Authors:  J E White; D Veale; D Fishwick; L Mitchell; P A Corris
Journal:  Thorax       Date:  1996-07       Impact factor: 9.139

Review 5.  Primary intestinal lymphangiectasia: Minireview.

Authors:  Sachin B Ingle; Chitra R Hinge Ingle
Journal:  World J Clin Cases       Date:  2014-10-16       Impact factor: 1.337

6.  Different patterns of lymphoscintigraphic findings in patients with intestinal lymphangiectasia.

Authors:  Y So; J K Chung; J K Seo; J S Ko; J Y Kim; D S Lee; M C Lee
Journal:  Nucl Med Commun       Date:  2001-11       Impact factor: 1.690

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Authors:  W L Tift; J K Lloyd
Journal:  Arch Dis Child       Date:  1975-04       Impact factor: 3.791

8.  Intestinal lymphangiectasia in children: a study of upper gastrointestinal endoscopic biopsies.

Authors:  C Abramowsky; V Hupertz; P Kilbridge; S Czinn
Journal:  Pediatr Pathol       Date:  1989

Review 9.  Primary intestinal lymphangiectasia (Waldmann's disease).

Authors:  Stéphane Vignes; Jérôme Bellanger
Journal:  Orphanet J Rare Dis       Date:  2008-02-22       Impact factor: 4.123

Review 10.  Intestinal Lymphangiectasia: Insights on Management and Literature Review.

Authors:  Mohamad J Alshikho; Joud M Talas; Salem I Noureldine; Saf Zazou; Aladdin Addas; Haitham Kurabi; Mahmoud Nasser
Journal:  Am J Case Rep       Date:  2016-07-21
  10 in total
  1 in total

1.  Individual approach for treatment of primary intestinal lymphangiectasia in children: single-center experience and review of the literature.

Authors:  Yiyoung Kwon; Eun Sil Kim; Yon Ho Choe; Mi Jin Kim
Journal:  BMC Pediatr       Date:  2021-01-07       Impact factor: 2.125
  1 in total

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