| Literature DB >> 28954117 |
Rafael Cavanellas Fraga1, Priscila Kakizaki2, Neusa Yuriko Sakai Valente2, Larissa Karine Leite Portocarrero2, Mônica Fernandes Senise Teixeira2, Priscilla Fernandes Senise3.
Abstract
Heerfordt-Waldenström syndrome is a rare subacute variant of sarcoidosis, characterized by enlargement of the parotid or salivary glands, facial nerve paralysis and anterior uveitis. Granulomas with a peripheral lymphocyte deficit are found in the anatomic pathology of affected organs. It is normally self-limiting, with cure achieved between 12 and 36 months, but some prolonged cases have been reported. Diagnosis of the syndrome is clinical, and treatment depends on the degree of systemic impairment. Oral corticosteroids represent the first line treatment option. The mortality rate ranges between 1 and 5% of cases.Entities:
Mesh:
Year: 2017 PMID: 28954117 PMCID: PMC5595615 DOI: 10.1590/abd1806-4841.20175211
Source DB: PubMed Journal: An Bras Dermatol ISSN: 0365-0596 Impact factor: 1.896