Warning: Undefined array key "mm" in /www/wwwroot/www.ai-bt.com/si.php on line 10 Deprecated: trim(): Passing null to parameter #1 ($string) of type string is deprecated in /www/wwwroot/www.ai-bt.com/si.php on line 10 Successful treatment of homozygous protein C deficiency by hepatic transplantation.

Literature DB >> 2893866

Successful treatment of homozygous protein C deficiency by hepatic transplantation.

J F Casella¹, J H Lewis, F A Bontempo, B J Zitelli, H Markel, T E Starzl.

Abstract

A child with homozygous protein C deficiency was treated at age 20 months by orthotopic hepatic transplantation. Postoperatively there was complete reconstitution of protein C activity and resolution of the thrombotic condition.

Entities: Disease Species

Mesh：

Substances：
Protein C

Year: 1988 PMID： 2893866 PMCID： PMC3091362 DOI： 10.1016/s0140-6736(88)91231-7

Source DB: PubMed Journal: Lancet ISSN： 0140-6736 Impact factor: 79.321

38 in total

1. Liver transplantation for type I glycogen storage disease.

Authors: J J Malatack; D N Finegold; S Iwatsuki; B W Shaw; J C Gartner; B J Zitelli; T Roe; T E Starzl
Journal: Lancet Date: 1983-05-14 Impact factor: 79.321

2. Protein C and the development of skin necrosis during anticoagulant therapy.

Authors: A W Broekmans; R M Bertina; E A Loeliger; V Hofmann; H G Klingemann
Journal: Thromb Haemost Date: 1983-06-28 Impact factor: 5.249

3. Deficiencies of protein C, an inhibitor of blood coagulation.

Authors: P M Mannucci; S Vigano
Journal: Lancet Date: 1982-08-28 Impact factor: 79.321

4. Protein C deficiency in two Austrian families.

Authors: I Pabinger-Fasching; R M Bertina; K Lechner; H Niessner; C Korninger
Journal: Thromb Haemost Date: 1983-12-30 Impact factor: 5.249

5. Homozygous protein C deficiency manifested by massive venous thrombosis in the newborn.

Authors: U Seligsohn; A Berger; M Abend; L Rubin; D Attias; A Zivelin; S I Rapaport
Journal: N Engl J Med Date: 1984-03-01 Impact factor: 91.245

6. The use of a functional and immunologic assay for plasma protein C in the study of the heterogeneity of congenital protein C deficiency.

Authors: R M Bertina; A W Broekmans; C Krommenhoek-van Es; A van Wijngaarden
Journal: Thromb Haemost Date: 1984-02-28 Impact factor: 5.249

7. Congenital protein C deficiency and venous thromboembolism. A study of three Dutch families.

Authors: A W Broekmans; J J Veltkamp; R M Bertina
Journal: N Engl J Med Date: 1983-08-11 Impact factor: 91.245

8. Inherited protein C deficiency and coumarin-responsive chronic relapsing purpura fulminans in a newborn infant.

Authors: H E Branson; J Katz; R Marble; J H Griffin
Journal: Lancet Date: 1983-11-19 Impact factor: 79.321

9. Determination of functional levels of protein C, an antithrombotic protein, using thrombin-thrombomodulin complex.

Authors: P C Comp; R R Nixon; C T Esmon
Journal: Blood Date: 1984-01 Impact factor: 22.113

10. Deficiency of protein C in congenital thrombotic disease.

Authors: J H Griffin; B Evatt; T S Zimmerman; A J Kleiss; C Wideman
Journal: J Clin Invest Date: 1981-11 Impact factor: 14.808

14 in total

1. Orthotopic liver transplantation in liver-based metabolic disorders.

Authors: A P Mowat
Journal: Eur J Pediatr Date: 1992 Impact factor: 3.183

Review 2. The present state of liver transplantation and the future prospects for intestinal transplantation.

Authors: T E Starzl
Journal: Immunol Invest Date: 1989 Jan-May Impact factor: 3.657

3. Surgical treatment of pulmonary hypertension in protein C deficiency.

Authors: N P Briffa; I Wilson; D B Clarke
Journal: Br Heart J Date: 1991-12

Review 4. Liver transplantation (1).

Authors: T E Starzl; A J Demetris; D Van Thiel
Journal: N Engl J Med Date: 1989-10-12 Impact factor: 91.245

5. Acute Budd-Chiari syndrome with hepatic failure and obstruction of the inferior vena cava as presenting manifestations of hereditary protein C deficiency.

Authors: M Bourlière; Y P Le Treut; D Arnoux; P Castellani; L Bordigoni; A Maillot; M Antoni; D Botta; B Pol; A P Gauthier
Journal: Gut Date: 1990-08 Impact factor: 23.059