Literature DB >> 28884425

Can a Neurosteroid Ameliorate Fragile X-Associated Tremor/Ataxia Syndrome?

Dejan B Budimirovic1.   

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Year:  2017        PMID: 28884425      PMCID: PMC5722773          DOI: 10.1007/s13311-017-0569-0

Source DB:  PubMed          Journal:  Neurotherapeutics        ISSN: 1878-7479            Impact factor:   7.620


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  24 in total

1.  N400-like magnetoencephalography responses modulated by semantic context, word frequency, and lexical class in sentences.

Authors:  Eric Halgren; Rupali P Dhond; Natalie Christensen; Cyma Van Petten; Ksenija Marinkovic; Jeffrey D Lewine; Anders M Dale
Journal:  Neuroimage       Date:  2002-11       Impact factor: 6.556

2.  The amygdala mediates the anxiolytic-like effect of the neurosteroid allopregnanolone in rat.

Authors:  Y Akwa; R H Purdy; G F Koob; K T Britton
Journal:  Behav Brain Res       Date:  1999-12       Impact factor: 3.332

3.  A Majority of FXTAS Cases Present with Intranuclear Inclusions Within Purkinje Cells.

Authors:  Jeanelle Ariza; Hailee Rogers; Angela Monterrubio; Adriana Reyes-Miranda; Paul J Hagerman; Verónica Martínez-Cerdeño
Journal:  Cerebellum       Date:  2016-10       Impact factor: 3.847

4.  Neuropathology of fragile X-associated tremor/ataxia syndrome (FXTAS).

Authors:  C M Greco; R F Berman; R M Martin; F Tassone; P H Schwartz; A Chang; B D Trapp; C Iwahashi; J Brunberg; J Grigsby; D Hessl; E J Becker; J Papazian; M A Leehey; R J Hagerman; P J Hagerman
Journal:  Brain       Date:  2005-12-05       Impact factor: 13.501

Review 5.  Hippocampal adult neurogenesis: Its regulation and potential role in spatial learning and memory.

Authors:  Claudia Lieberwirth; Yongliang Pan; Yan Liu; Zhibin Zhang; Zuoxin Wang
Journal:  Brain Res       Date:  2016-05-10       Impact factor: 3.252

6.  Two FMR1 premutation cases without nuclear inclusions.

Authors:  Verónica Martínez-Cerdeño; Mirna Lechpammer; Paul J Hagerman; Randi Hagerman
Journal:  Mov Disord       Date:  2017-06-01       Impact factor: 10.338

7.  Memantine for fragile X-associated tremor/ataxia syndrome: a randomized, double-blind, placebo-controlled trial.

Authors:  Andreea L Seritan; Danh V Nguyen; Yi Mu; Flora Tassone; James A Bourgeois; Andrea Schneider; Jennifer B Cogswell; Kylee R Cook; Maureen A Leehey; Jim Grigsby; John M Olichney; Patrick E Adams; Wendi Legg; Lin Zhang; Paul J Hagerman; Randi J Hagerman
Journal:  J Clin Psychiatry       Date:  2014-03       Impact factor: 4.384

Review 8.  Fragile X-associated tremor/ataxia syndrome: clinical features, genetics, and testing guidelines.

Authors:  Elizabeth Berry-Kravis; Liane Abrams; Sarah M Coffey; Deborah A Hall; Claudia Greco; Louise W Gane; Jim Grigsby; James A Bourgeois; Brenda Finucane; Sebastien Jacquemont; James A Brunberg; Lin Zhang; Janet Lin; Flora Tassone; Paul J Hagerman; Randi J Hagerman; Maureen A Leehey
Journal:  Mov Disord       Date:  2007-10-31       Impact factor: 10.338

9.  Fragile X-associated tremor/ataxia syndrome: influence of the FMR1 gene on motor fiber tracts in males with normal and premutation alleles.

Authors:  Jun Yi Wang; David Hessl; Andrea Schneider; Flora Tassone; Randi J Hagerman; Susan M Rivera
Journal:  JAMA Neurol       Date:  2013-08       Impact factor: 18.302

Review 10.  Updated report on tools to measure outcomes of clinical trials in fragile X syndrome.

Authors:  Dejan B Budimirovic; Elizabeth Berry-Kravis; Craig A Erickson; Scott S Hall; David Hessl; Allan L Reiss; Margaret K King; Leonard Abbeduto; Walter E Kaufmann
Journal:  J Neurodev Disord       Date:  2017-06-12       Impact factor: 4.025

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  1 in total

1.  Clinical and Molecular Correlates of Abnormal Changes in the Cerebellum and Globus Pallidus in Fragile X Premutation.

Authors:  Jun Yi Wang; Jim Grigsby; Diego Placido; Hongjiang Wei; Flora Tassone; Kyoungmi Kim; David Hessl; Susan M Rivera; Randi J Hagerman
Journal:  Front Neurol       Date:  2022-02-08       Impact factor: 4.003

  1 in total

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