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10 in total

1. Quantitative correlation between the residual activity of beta-hexosaminidase A and arylsulfatase A and the severity of the resulting lysosomal storage disease.

Authors: P Leinekugel; S Michel; E Conzelmann; K Sandhoff
Journal: Hum Genet Date: 1992-03 Impact factor: 4.132

Review 2. The anomalous kinetics of sulphatase A.

Authors: A B Roy; T J Mantle
Journal: Biochem J Date: 1989-08-01 Impact factor: 3.857

3. Sphingolipid activator protein 1 deficiency in metachromatic leucodystrophy with normal arylsulphatase A activity. A clinical, morphological, biochemical, and immunological study.

Authors: W Schlote; K Harzer; H Christomanou; B C Paton; B Kustermann-Kuhn; B Schmid; J Seeger; U Beudt; I Schuster; U Langenbeck
Journal: Eur J Pediatr Date: 1991-06 Impact factor: 3.183

4. Diagnosis and prevention of lysosomal storage diseases in Russia.

Authors: K D Krasnopolskaya; T V Mirenburg; E L Aronovich; T V Lebedeva; O N Odinokova; N A Demina; V M Kozlova; M I Kuznetsov
Journal: J Inherit Metab Dis Date: 1993 Impact factor: 4.982

5. Metabolism of GM1 ganglioside in cultured skin fibroblasts: anomalies in gangliosidoses, sialidoses, and sphingolipid activator protein (SAP, saposin) 1 and prosaposin deficient disorders.

Authors: B Schmid; B C Paton; K Sandhoff; K Harzer
Journal: Hum Genet Date: 1992-07 Impact factor: 4.132

6. Identification of a lysosomal protein causing lipid transfer, using a fluorescence assay designed to monitor membrane fusion between rat liver endosomes and lysosomes.

Authors: T Kuwana; B M Mullock; J P Luzio
Journal: Biochem J Date: 1995-06-15 Impact factor: 3.857

7. Action of alpha-L-fucoside from Octopus vulgaris hepatopancreas on phospholipid vesicles containing the fucosylated ganglioside FucGM1.

Authors: A Giuliani; P Palestini; A D'Aniello; M Masserini
Journal: Glycoconj J Date: 1993-12 Impact factor: 2.916

Review 8. [Sphingolipid storage diseases of the central nervous system: bases of biochemical and clinical heterogeneity].

Authors: K Sandhoff; L Quintern
Journal: Naturwissenschaften Date: 1988-03

9. Prosaposin deficiency: further characterization of the sphingolipid activator protein-deficient sibs. Multiple glycolipid elevations (including lactosylceramidosis), partial enzyme deficiencies and ultrastructure of the skin in this generalized sphingolipid storage disease.

Authors: V Bradová; F Smíd; B Ulrich-Bott; W Roggendorf; B C Paton; K Harzer
Journal: Hum Genet Date: 1993-09 Impact factor: 4.132

10. Requirement of GM2 ganglioside activator for phospholipase D activation.

Authors: S Nakamura; T Akisue; H Jinnai; T Hitomi; S Sarkar; N Miwa; T Okada; K Yoshida; S Kuroda; U Kikkawa; Y Nishizuka
Journal: Proc Natl Acad Sci U S A Date: 1998-10-13 Impact factor: 11.205

10 in total