Literature DB >> 28766559

Long-term treatment of phenylketonuria with a new medical food containing large neutral amino acids.

D Concolino, I Mascaro, M T Moricca, G Bonapace, K Matalon, J Trapasso, G Radhakrishnan, C Ferrara, R Matalon, P Strisciuglio.   

Abstract

This corrects the article DOI: 10.1038/ejcn.2016.166.

Entities:  

Year:  2017        PMID: 28766559      PMCID: PMC5543251          DOI: 10.1038/ejcn.2017.98

Source DB:  PubMed          Journal:  Eur J Clin Nutr        ISSN: 0954-3007            Impact factor:   4.016


Correction to: European Journal of Clinical Nutrition (2017); 71 (1); 51-55; doi: 10.1038/ejcn.2016.166; published online 14th September 2016 Since the publication of the article, the authors have noticed an error in Table 1. The corrected table can be found below.
Table 1

Composition of PheLNAA for 100 g powder

Energy kcal293.50 Vitamins
kJ1241.26 Amcg1300
 D3mcg15.5
Protein equivalentg48.94 Emg20
Carbohydratesg15.74 K1mcg113
 Sugarsg12.46 Cmg100
Fatsg2.58 B1mg1.5
 DHAmg610 B2mg1.8
 B6mg5.4
 B12mcg9
Amino Acids g61.73 Biotinmcg150
 Arginineg2.79 Cholinemg650
 Aspartic Acidg2.36 Inositolmg125
 Glutamineg3.52 Niacinmg20
 Isoleucineg3.33 Folic acidmcg750
 Leucineg9.79 Pantothenic acidmg8.8
 Lysineg5.70 Minerals
 Methionineg0.97 Calciummg1600
 Prolineg3.45 Chromiummcg40
 Threonineg3.15 Coppermg1.5
 Tryptophang3.33 Iodinemcg200
 Tyrosineg18.79 Ironmg20
 Valineg3.33 Magnesiummg500
 Hystidineg1.21 Manganesemg3
 Molybdenummcg90
 Phosphorousmg1250
 Seleniummcg75
 Sodiummg40
 Zincmg15
Lutein mg12

Abbreviation: PheLNAA, phenylalanine-neutral amino acid.

Composition of PheLNAA for 100 g powder Abbreviation: PheLNAA, phenylalanine-neutral amino acid. The authors apologise for any inconvenience caused by this error.
  4 in total

1.  Starting the conversation on gene therapy for phenylketonuria: Current perspectives of patients, caregivers, and advocates.

Authors:  Debra S Regier; Agata Bąk; Heather Bausell; Emer O'Reilly; Lex M Cowsert
Journal:  Mol Genet Metab Rep       Date:  2022-03-08

2.  Large Neutral Amino Acids (LNAAs) Supplementation Improves Neuropsychological Performances in Adult Patients with Phenylketonuria.

Authors:  Iris Scala; Maria Pia Riccio; Maria Marino; Carmela Bravaccio; Giancarlo Parenti; Pietro Strisciuglio
Journal:  Nutrients       Date:  2020-04-15       Impact factor: 5.717

3.  Large neutral amino acid status in association with P:T ratio and diet in adult and pediatric patients with phenylketonuria.

Authors:  Teresa D Douglas; Anita M Nucci; Ann M Berry; Sarah T Henes; Rani H Singh
Journal:  JIMD Rep       Date:  2019-09-16

4.  Beneficial Effects of Slow-Release Large Neutral Amino Acids after a Phenylalanine Oral Load in Patients with Phenylketonuria.

Authors:  Iris Scala; Daniela Concolino; Anna Nastasi; Giulia Esposito; Daniela Crisci; Simona Sestito; Stefania Ferraro; Lucia Albano; Margherita Ruoppolo; Giancarlo Parenti; Pietro Strisciuglio
Journal:  Nutrients       Date:  2021-11-10       Impact factor: 5.717

  4 in total

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