Literature DB >> 2876234

Enzyme replacement in nervous tissue after allogeneic bone-marrow transplantation for fucosidosis in dogs.

R M Taylor, B R Farrow, G J Stewart, P J Healy.   

Abstract

Bone-marrow transplantation after total lymphoid irradiation in an alpha-L-fucosidase-deficient dog raised the enzyme activity in both visceral and neural tissues with consequent reduction in the severity of storage lesions. These results offer hope that early marrow transplantation may prevent the development of disease in neurovisceral storage disorders.

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Year:  1986        PMID： 2876234     DOI： 10.1016/s0140-6736(86)90299-0

Source DB:  PubMed          Journal:  Lancet        ISSN： 0140-6736            Impact factor:   79.321


  14 in total

Review 1.  Enzyme-replacement therapy: problems and prospects.

Authors:  B Rademaker; J Raber
Journal:  Pharm Weekbl Sci       Date:  1989-10-20

2.  Bone marrow transplantation in the treatment of alpha-mannosidosis.

Authors:  A Will; A Cooper; C Hatton; I B Sardharwalla; D I Evans; R F Stevens
Journal:  Arch Dis Child       Date:  1987-10       Impact factor: 3.791

3.  Canine alpha-L-fucosidase in relation to the enzymic defect and storage products in canine fucosidosis.

Authors:  C Barker; A Dell; M Rogers; J A Alhadeff; B Winchester
Journal:  Biochem J       Date:  1988-09-15       Impact factor: 3.857

Review 4.  Transplantation of fetal cells and tissue: an overview.

Authors:  A Fine
Journal:  CMAJ       Date:  1994-11-01       Impact factor: 8.262

Review 5.  Displacement bone marrow transplantation for some inborn errors.

Authors:  J R Hobbs
Journal:  J Inherit Metab Dis       Date:  1990       Impact factor: 4.982

6.  Murine mucopolysaccharidosis type VII: long term therapeutic effects of enzyme replacement and enzyme replacement followed by bone marrow transplantation.

Authors:  M S Sands; C Vogler; A Torrey; B Levy; B Gwynn; J Grubb; W S Sly; E H Birkenmeier
Journal:  J Clin Invest       Date:  1997-04-01       Impact factor: 14.808

7.  Management of women with mild and moderate cervical dyskaryosis.

Authors:  G Flannelly; D Anderson; H C Kitchener; E M Mann; M Campbell; P Fisher; F Walker; A A Templeton
Journal:  BMJ       Date:  1994-05-28

8.  Caprine beta-D-mannosidosis: characterization of a model lysosomal storage disorder.

Authors:  R D Pearce; J W Callahan; P B Little; L R Klunder; J T Clarke
Journal:  Can J Vet Res       Date:  1990-01       Impact factor: 1.310

9.  Long-term effects of bone marrow transplantation on lysosomal enzyme replacement in beta-glucuronidase-deficient mice.

Authors:  G Bou-Gharios; G Adams; P Pace; I Olsen
Journal:  J Inherit Metab Dis       Date:  1992       Impact factor: 4.982

Review 10.  Advances in the molecular genetics of metachromatic leukodystrophy.

Authors:  V Gieselmann; K von Figura
Journal:  J Inherit Metab Dis       Date:  1990       Impact factor: 4.982
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