Literature DB >> 2870324

Dangers of non-compliance in Wilson's disease.

J M Walshe, A K Dixon.   

Abstract

A patient who presented with severe hepatic Wilson's disease at age 14 responded well to treatment with penicillamine and remained in good health for a further 20 years, although she became somewhat careless about her medication towards the end of this period. Finally she abandoned treatment altogether and died of hepatic failure 2 1/2 years later. Abdominal computed tomography showed that the main structural damage to the liver occurred in this relatively short period of non-compliance after over 20 years of normal health on maintenance penicillamine therapy.

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Year:  1986        PMID: 2870324     DOI: 10.1016/s0140-6736(86)90949-9

Source DB:  PubMed          Journal:  Lancet        ISSN: 0140-6736            Impact factor:   79.321


  13 in total

Review 1.  ACP Best Practice No 163. Wilson's disease: acute and presymptomatic laboratory diagnosis and monitoring.

Authors:  D Gaffney; G S Fell; D S O'Reilly
Journal:  J Clin Pathol       Date:  2000-11       Impact factor: 3.411

2.  Report of the ASFA apheresis registry study on Wilson's disease.

Authors:  Huy P Pham; Joseph Schwartz; Laura Cooling; Jan C Hofmann; Haewon C Kim; Shanna Morgan; Monica B Pagano; Jennifer Schneiderman; Jeffrey L Winters; Chisa Yamada; Edward C C Wong; Yanyun Wu
Journal:  J Clin Apher       Date:  2015-08-14       Impact factor: 2.821

3.  Wilson's disease in Scotland.

Authors:  R H Park; P McCabe; G S Fell; R I Russell
Journal:  Gut       Date:  1991-12       Impact factor: 23.059

Review 4.  A review and current perspective on Wilson disease.

Authors:  Mallikarjun Patil; Keyur A Sheth; Adarsh C Krishnamurthy; Harshad Devarbhavi
Journal:  J Clin Exp Hepatol       Date:  2013-07-06

Review 5.  Evolving perspectives in Wilson disease: diagnosis, treatment and monitoring.

Authors:  Karl Heinz Weiss; Wolfgang Stremmel
Journal:  Curr Gastroenterol Rep       Date:  2012-02

Review 6.  Copper and liver disease.

Authors:  D M Danks
Journal:  Eur J Pediatr       Date:  1991-01       Impact factor: 3.183

7.  Dietary copper triggers onset of fulminant hepatitis in the Long-Evans cinnamon rat model.

Authors:  Ramsi Siaj; Vanessa Sauer; Sandra Stöppeler; Hans-Ullrich Spiegel; Gabriele Köhler; Andree Zibert; Hartmut H J Schmidt
Journal:  World J Gastroenterol       Date:  2012-10-21       Impact factor: 5.742

Review 8.  Triethylene tetramine dihydrochloride (trientine) in children with Wilson disease: experience at King's College Hospital and review of the literature.

Authors:  Rachel M Taylor; Yuan Chen; Anil Dhawan
Journal:  Eur J Pediatr       Date:  2008-12-09       Impact factor: 3.183

Review 9.  The Pragmatic Treatment of Wilson's Disease.

Authors:  Annu Aggarwal; Mohit Bhatt
Journal:  Mov Disord Clin Pract       Date:  2014-04-10

Review 10.  Wilson's disease and other neurological copper disorders.

Authors:  Oliver Bandmann; Karl Heinz Weiss; Stephen G Kaler
Journal:  Lancet Neurol       Date:  2015-01       Impact factor: 44.182

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