Felipe H Sanders1,2, Bryan A Edwards3,4, Matthew Fusco2,5, Rod J Oskouian1, R Shane Tubbs1,2, James M Johnston1,2. 1. Seattle Science Foundation, Seattle, WA, USA. 2. Pediatric Neurosurgery, Children's of Alabama, Birmingham, AL, USA. 3. Department of Anatomical Sciences, St. George's University, St. George's, Grenada. bedward1@sgu.edu. 4. , 11545 95A Ave, Delta, BC, V4C 3V4, Canada. bedward1@sgu.edu. 5. Department of Neurosurgery, Vanderbilt University, Nashville, TN, USA.
Abstract
INTRODUCTION: Sinus pericranii is a rare vascular malformation that connects the intracranial dural sinuses to the extracranial venous drainage system and is caused by either trauma or congenital defects. Although the majority of these vascular structures are due to trauma, some are congenital. CASE REPORT: Herein, we report a 5-month-old patient with a very large and fluctuating subcutaneous mass over the occiput and the diagnosis of Crouzon's syndrome. The child presented with a large midline mass that on imaging, connected to the underlying torcular and was diagnosed as a sinus pericranii. At long-term follow-up and without operative intervention, the sinus pericranii resolved. This uncommon relationship is reviewed. CONCLUSION: Premature closure of posterior fossa sutures as part of Crouzon's syndrome can present with large sinus pericranii. Such subcutaneous swellings might resolve spontaneously.
INTRODUCTION: Sinus pericranii is a rare vascular malformation that connects the intracranial dural sinuses to the extracranial venous drainage system and is caused by either trauma or congenital defects. Although the majority of these vascular structures are due to trauma, some are congenital. CASE REPORT: Herein, we report a 5-month-old patient with a very large and fluctuating subcutaneous mass over the occiput and the diagnosis of Crouzon's syndrome. The child presented with a large midline mass that on imaging, connected to the underlying torcular and was diagnosed as a sinus pericranii. At long-term follow-up and without operative intervention, the sinus pericranii resolved. This uncommon relationship is reviewed. CONCLUSION: Premature closure of posterior fossa sutures as part of Crouzon's syndrome can present with large sinus pericranii. Such subcutaneous swellings might resolve spontaneously.
Authors: Mary Sheu; Greg Fauteux; Howard Chang; William Taylor; Edward Stopa; Leslie Robinson-Bostom Journal: J Am Acad Dermatol Date: 2002-06 Impact factor: 11.527
Authors: Carlo Gandolfo; Timo Krings; Hortensia Alvarez; Augustin Ozanne; Meike Schaaf; Carlos E Baccin; Wen-Yuan Zhao; Pierre Lasjaunias Journal: Neuroradiology Date: 2007-02-07 Impact factor: 2.995