Literature DB >> 28580220

Pancreatic lipomatosis in cystic fibrosis: Rare manifestation of an uncommon disease.

Harshal S Mandavdhare1, Amit Kumar1, Vishal Sharma1, Surinder S Rana1.   

Abstract

Cystic fibrosis is deemed to be uncommon in India. The presentation is usually in the childhood although more cases are now being recognized in adolescence and adulthood. We report a case of an adolescent male who had been treated for recurrent pulmonary infections and received anti-tubercular therapy for a possible diagnosis of sputum negative pulmonary tuberculosis and was evaluated for steatorrhea. The presence of pancreatic exocrine insufficiency along with pancreatic lipomatosis suggested the diagnosis of cystic fibrosis.

Entities:  

Keywords:  Cystic fibrosis; bronchiectasis; endoscopic ultrasound; pancreatic exocrine insufficiency; steatorrhea

Year:  2017        PMID: 28580220      PMCID: PMC5451751          DOI: 10.5582/irdr.2017.01008

Source DB:  PubMed          Journal:  Intractable Rare Dis Res        ISSN: 2186-3644


  5 in total

Review 1.  Cystic fibrosis in India: a systematic review.

Authors:  Tester F Ashavaid; Rani Raghavan; Pradnya Dhairyawan; Shweta Bhawalkar
Journal:  J Assoc Physicians India       Date:  2012-08

2.  Pancreatic Lipomatosis: Complete Replacement of Pancreas by Fat.

Authors:  Paurush Ambesh; Hira Lal
Journal:  J Clin Diagn Res       Date:  2015-10-01

3.  Imaging changes in the pancreas in cystic fibrosis: a retrospective evaluation of 55 cases seen over a period of 9 years.

Authors:  J Feigelson; Y Pécau; M Poquet; P Terdjman; J Carrère; J P Chazalette; C Ferec
Journal:  J Pediatr Gastroenterol Nutr       Date:  2000-02       Impact factor: 2.839

Review 4.  New horizons for cystic fibrosis treatment.

Authors:  Isabelle Fajac; Kris De Boeck
Journal:  Pharmacol Ther       Date:  2016-12-01       Impact factor: 12.310

5.  Total pancreatic lipomatosis with malabsorption syndrome.

Authors:  Rama Anand; Mahender K Narula; Vikas Chaudhary; Rohini Agrawal
Journal:  Indian J Endocrinol Metab       Date:  2011-01
  5 in total
  1 in total

1.  Surgery for Ampullary Cancer in a Patient with Pancreatic Lipomatosis Caused by Cystic Fibrosis.

Authors:  Nienke E Vuurberg; Ilsalien Bakker; Anne Loes van den Boom; Robbert J de Haas; Evelien W Duiker; Marius C van den Heuvel; Joost M Klaase
Journal:  Case Rep Gastroenterol       Date:  2020-12-15
  1 in total

北京卡尤迪生物科技股份有限公司 © 2022-2023.