Literature DB >> 28571197

Cardiac Amyloidosis, An Infiltrative Heart Disease Presenting as Arrhythmia-A Case Report.

B Magesh1, Deepak Kadeli2, Sunil Bohra3, V Krishnaprasath2, R Keshava4.   

Abstract

Cardiac amyloidosis is a manifestation of amyloidosis which is a multisystem disorder. This is difficult to diagnose, rare disease which eventually leads to the mortality. Diagnosis requires a high index of clinical suspicion along with echocardiographic clues like, diastolic dysfunction, bi-atrial enlargement and ventricular thickening. Treatment is mainly supportive with disappointing outcomes. We present a case of systemic amyloidosis with negative congo red staining, presenting with predominantly cardiac features.

Entities:  

Keywords:  Bi-atrial enlargement; Congo red staining; Macroglossia; Ventricular thickening

Year:  2017        PMID: 28571197      PMCID: PMC5449843          DOI: 10.7860/JCDR/2017/24698.9661

Source DB:  PubMed          Journal:  J Clin Diagn Res        ISSN: 0973-709X


  13 in total

Review 1.  Diagnosis and management of the cardiac amyloidoses.

Authors:  Rodney H Falk
Journal:  Circulation       Date:  2005-09-27       Impact factor: 29.690

2.  Cardiac amyloidosis--two case reports with variable presentation.

Authors:  Bishav Mohan; Shibba Takkar Chhabra; Rohit Tandon; Naveen K Gupta; Naved Aslam; Naresh K Sood; Gurpreet S Wander
Journal:  J Assoc Physicians India       Date:  2011-04

Review 3.  Amyloidotic cardiomyopathy: multidisciplinary approach to diagnosis and treatment.

Authors:  David C Seldin; John L Berk; Flora Sam; Vaishali Sanchorawala
Journal:  Heart Fail Clin       Date:  2011-05-20       Impact factor: 3.179

4.  Case report: isolated cardiac amyloidosis: an enigma unravelled.

Authors:  Umair Khalid; Omar Awar; Gordana Verstovsek; Benjamin Cheong; Sarvari Venkata Yellapragada; Hani Jneid; Anita Deswal; Salim S Virani
Journal:  Methodist Debakey Cardiovasc J       Date:  2015 Jan-Mar

5.  Diagnosis and typing of systemic amyloidosis: The role of abdominal fat pad fine needle aspiration biopsy.

Authors:  Ruba A Halloush; Elena Lavrovskaya; Dina R Mody; Donna Lager; Luan Truong
Journal:  Cytojournal       Date:  2010-01-15       Impact factor: 2.091

6.  Cardiac amyloidosis presenting with prolonged QT interval and recurrent polymorphic ventricular tachycardia.

Authors:  Nisha A Gilotra; Grant V Chow; Oscar H Cingolani
Journal:  Tex Heart Inst J       Date:  2013

7.  [A case of primary cardiac amyloidosis with amyloid A protein].

Authors:  A Aouda; T Toyozaki; T Saito; K Yorimitsu; A Miyazaki; F Deguchi; Y Inagaki
Journal:  Kokyu To Junkan       Date:  1993-01

Review 8.  Evaluation and management of the cardiac amyloidosis.

Authors:  Joseph B Selvanayagam; Philip N Hawkins; Biju Paul; Saul G Myerson; Stefan Neubauer
Journal:  J Am Coll Cardiol       Date:  2007-11-13       Impact factor: 24.094

Review 9.  Transthyretin (TTR) cardiac amyloidosis.

Authors:  Frederick L Ruberg; John L Berk
Journal:  Circulation       Date:  2012-09-04       Impact factor: 29.690

Review 10.  Amyloid in surgical pathology.

Authors:  Christoph Röcken; Knut Sletten
Journal:  Virchows Arch       Date:  2003-06-11       Impact factor: 4.064

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